Literature DB >> 35399694

A Treatment-free Interval Allowed by Ponatinib as Fourth-line Therapy.

Anna Bulla1, Uros Markovic1, Claudia Bellofiore1, Stefania Stella2, Concetta Conticello1, Francesco DI Raimondo1, Fabio Stagno1.   

Abstract

Background: The third-generation tyrosine kinase inhibitor ponatinib has demonstrated high clinical efficacy in the setting of patients with resistant chronic phase chronic myeloid leukemia (CML), also inducing deep molecular responses. However, ponatinib-related cardiovascular toxicities make management challenging, especially of those patients with CML with previous cardiovascular comorbidities. Case Report: We report on the efficacy of ponatinib treatment used as fourth-line therapy in a 55-year-old woman affected by significant comorbidities (mainly cardiovascular) present before the diagnosis of CML. Ponatinib therapy induced a rapid and excellent clinical response, with the achievement of a durable deep molecular response that allowed us to propose a strategy of treatment discontinuation in order to reduce drug-related toxicities.
Conclusion: A strategy of a treatment-free interval might represent a useful clinical tool in those patients with CML who achieve a durable deep molecular response but are also affected by significant comorbidities in order to minimize the risk of ponatinib-related toxicities. Copyright 2021, International Institute of Anticancer Research.

Entities:  

Keywords:  CML therapy; Chronic myeloid leukemia; cardiovascular adverse events; ponatinib; treatment free interval

Year:  2021        PMID: 35399694      PMCID: PMC8962775          DOI: 10.21873/cdp.10003

Source DB:  PubMed          Journal:  Cancer Diagn Progn        ISSN: 2732-7787


  17 in total

1.  NCCN Guidelines Updates: Discontinuing TKI Therapy in the Treatment of Chronic Myeloid Leukemia.

Authors:  Neil P Shah
Journal:  J Natl Compr Canc Netw       Date:  2019-05-01       Impact factor: 11.908

2.  Ponatinib as second-line treatment in chronic phase chronic myeloid leukemia patients in real-life practice.

Authors:  Massimo Breccia; Elisabetta Abruzzese; Fausto Castagnetti; Massimiliano Bonifacio; Domenica Gangemi; Federica Sorà; Alessandra Iurlo; Luigiana Luciano; Antonella Gozzini; Massimo Gentile; Monica Bocchia; Debora Luzi; Alessandro Maggi; Nicola Sgherza; Alessandro Isidori; Monica Crugnola; Patrizia Pregno; Anna Rita Scortechini; Isabella Capodanno; Michele Pizzuti; Robin Foà
Journal:  Ann Hematol       Date:  2018-04-19       Impact factor: 3.673

3.  Ponatinib efficacy and safety in Philadelphia chromosome-positive leukemia: final 5-year results of the phase 2 PACE trial.

Authors:  Jorge E Cortes; Dong-Wook Kim; Javier Pinilla-Ibarz; Philipp D le Coutre; Ronald Paquette; Charles Chuah; Franck E Nicolini; Jane F Apperley; H Jean Khoury; Moshe Talpaz; Daniel J DeAngelo; Elisabetta Abruzzese; Delphine Rea; Michele Baccarani; Martin C Müller; Carlo Gambacorti-Passerini; Stephanie Lustgarten; Victor M Rivera; Frank G Haluska; François Guilhot; Michael W Deininger; Andreas Hochhaus; Timothy P Hughes; Neil P Shah; Hagop M Kantarjian
Journal:  Blood       Date:  2018-03-22       Impact factor: 22.113

Review 4.  Discontinuation of TKI therapy and 'functional' cure for CML.

Authors:  François-Xavier Mahon
Journal:  Best Pract Res Clin Haematol       Date:  2016-10-20       Impact factor: 3.020

Review 5.  On the road to treatment-free remission in chronic myeloid leukemia: what about 'the others'?

Authors:  Fabio Stagno; Massimo Breccia; Francesco Di Raimondo
Journal:  Expert Rev Anticancer Ther       Date:  2020-10-08       Impact factor: 4.512

6.  Managing chronic myeloid leukemia for treatment-free remission: a proposal from the GIMEMA CML WP.

Authors:  Michele Baccarani; Elisabetta Abruzzese; Vincenzo Accurso; Francesco Albano; Mario Annunziata; Sara Barulli; Germana Beltrami; Micaela Bergamaschi; Gianni Binotto; Monica Bocchia; Giovanni Caocci; Isabella Capodanno; Francesco Cavazzini; Michele Cedrone; Marco Cerrano; Monica Crugnola; Mariella D'Adda; Chiara Elena; Carmen Fava; Paola Fazi; Claudio Fozza; Sara Galimberti; Valentina Giai; Antonella Gozzini; Gabriele Gugliotta; Alessandra Iurlo; Gaetano La Barba; Luciano Levato; Alessandro Lucchesi; Luigia Luciano; Francesca Lunghi; Monia Lunghi; Michele Malagola; Roberto Marasca; Bruno Martino; Angela Melpignano; Maria Cristina Miggiano; Enrico Montefusco; Caterina Musolino; Fausto Palmieri; Patrizia Pregno; Davide Rapezzi; Giovanna Rege-Cambrin; Serena Rupoli; Marzia Salvucci; Rosaria Sancetta; Simona Sica; Raffaele Spadano; Fabio Stagno; Mario Tiribelli; Simona Tomassetti; Elena Trabacchi; Massimiliano Bonifacio; Massimo Breccia; Fausto Castagnetti; Fabrizio Pane; Domenico Russo; Giuseppe Saglio; Simona Soverini; Paolo Vigneri; Gianantonio Rosti
Journal:  Blood Adv       Date:  2019-12-23

7.  Chronic myeloid leukemia: 2020 update on diagnosis, therapy and monitoring.

Authors:  Elias Jabbour; Hagop Kantarjian
Journal:  Am J Hematol       Date:  2020-04-10       Impact factor: 10.047

Review 8.  European LeukemiaNet recommendations for the management and avoidance of adverse events of treatment in chronic myeloid leukaemia.

Authors:  J L Steegmann; M Baccarani; M Breccia; L F Casado; V García-Gutiérrez; A Hochhaus; D-W Kim; T D Kim; H J Khoury; P Le Coutre; J Mayer; D Milojkovic; K Porkka; D Rea; G Rosti; S Saussele; R Hehlmann; R E Clark
Journal:  Leukemia       Date:  2016-04-28       Impact factor: 11.528

9.  Observational study of chronic myeloid leukemia Italian patients who discontinued tyrosine kinase inhibitors in clinical practice.

Authors:  Carmen Fava; Giovanna Rege-Cambrin; Irene Dogliotti; Marco Cerrano; Paola Berchialla; Matteo Dragani; Gianantonio Rosti; Fausto Castagnetti; Gabriele Gugliotta; Bruno Martino; Carlo Gambacorti-Passerini; Elisabetta Abruzzese; Chiara Elena; Patrizia Pregno; Antonella Gozzini; Isabella Capodanno; Micaela Bergamaschi; Monica Crugnola; Monica Bocchia; Sara Galimberti; Davide Rapezzi; Alessandra Iurlo; Daniele Cattaneo; Roberto Latagliata; Massimo Breccia; Michele Cedrone; Marco Santoro; Mario Annunziata; Luciano Levato; Fabio Stagno; Francesco Cavazzini; Nicola Sgherza; Valentina Giai; Luigia Luciano; Sabina Russo; Pellegrino Musto; Giovanni Caocci; Federica Sorà; Francesco Iuliano; Francesca Lunghi; Giorgina Specchia; Fabrizio Pane; Dario Ferrero; Michele Baccarani; Giuseppe Saglio
Journal:  Haematologica       Date:  2019-02-28       Impact factor: 9.941

10.  Discontinuation of tyrosine kinase inhibitors in chronic myeloid leukemia: when and for whom?

Authors:  Ehab Atallah; Charles A Schiffer
Journal:  Haematologica       Date:  2020-12-01       Impact factor: 9.941

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