Literature DB >> 35059049

A disease beyond the aortic arch presenting as a hypertensive emergency.

Kashyap Shah1, Marc Kervin Antoine2, Raymond Durkin2, Raymond J Fitzpatrick3.   

Abstract

The mid-aortic syndrome, also known as mid-aortic dysplastic syndrome or coarctation of aorta, is a rare clinical entity due to the narrowing of the distal thoracic and/or abdominal aorta and its branches. It has various causes including congenital or acquired although idiopathic is the most common cause. It is more common in children and adolescents. Here we present a unique case of a 52-year-old woman who presented with shortness of breath, chest pain, and hypertensive emergency and was found to have high-grade mid-aortic stenosis which was successfully managed with surgery with no post-operative complications and complete resolution of her symptoms. <Learning objective: Mid-aortic syndrome (MAS) is a rare syndrome with various causes and presentations. It is associated with significant morbidity and mortality if left untreated. MAS can be managed symptomatically or surgically which requires taking multiple factors (age, severity, location and length of stenosis, severity of symptoms, previous response to medical therapy, end-organ damage, and visceral vessels involvement) into consideration including patient's own preferences.>.
© 2021 Japanese College of Cardiology. Published by Elsevier Ltd. All rights reserved.

Entities:  

Keywords:  Coarctation of aorta; Mid-aortic dysplastic syndrome; Mid-aortic syndrome

Year:  2021        PMID: 35059049      PMCID: PMC8758586          DOI: 10.1016/j.jccase.2021.03.007

Source DB:  PubMed          Journal:  J Cardiol Cases        ISSN: 1878-5409


  5 in total

Review 1.  Disease Beyond the Arch: A Systematic Review of Middle Aortic Syndrome in Childhood.

Authors:  Rawan K Rumman; Cheri Nickel; Mina Matsuda-Abedini; Armando J Lorenzo; Valerie Langlois; Seetha Radhakrishnan; Joao Amaral; Luc Mertens; Rulan S Parekh
Journal:  Am J Hypertens       Date:  2015-01-27       Impact factor: 2.689

Review 2.  Middle aortic syndrome: from presentation to contemporary open surgical and endovascular treatment.

Authors:  Konstantinos T Delis; Peter Gloviczki
Journal:  Perspect Vasc Surg Endovasc Ther       Date:  2005-09

3.  Clinical Characteristics and Long-Term Outcomes of Midaortic Syndrome.

Authors:  Ritesh S Patel; Stephanie Nguyen; Michelle T Lee; Matt D Price; Heidi Krause; Van Thi Thanh Truong; Harleen K Sandhu; Kristofer M Charlton-Ouw; Scott A LeMaire; Joseph S Coselli; Siddharth K Prakash
Journal:  Ann Vasc Surg       Date:  2020-01-07       Impact factor: 1.466

4.  Midaortic syndrome: 30 years of experience with medical, endovascular and surgical management.

Authors:  Diego Porras; Deborah R Stein; Michael A Ferguson; Gulraiz Chaudry; Ahmad Alomari; Khashayar Vakili; Steven J Fishman; James E Lock; Heung B Kim
Journal:  Pediatr Nephrol       Date:  2013-06-18       Impact factor: 3.714

5.  Coarctation of the abdominal aorta.

Authors:  T M Bergamini; J D Bernard; C Mavroudis; C L Backer; A J Muster; J D Richardson
Journal:  Ann Vasc Surg       Date:  1995-07       Impact factor: 1.466

  5 in total

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