Literature DB >> 35043222

Good therapeutic response to infliximab in a case of Susac syndrome refractory to immunotherapies including tocilizumab.

Stanislas Demuth1, Thomas Bogdan1, Laurent Kremer1, Livia Lanotte1, Nicolas Collongues1, Jérôme de Seze1, Kévin Bigaut2.   

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Year:  2022        PMID: 35043222     DOI: 10.1007/s00415-021-10922-x

Source DB:  PubMed          Journal:  J Neurol        ISSN: 0340-5354            Impact factor:   6.682


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  20 in total

Review 1.  Diagnostic criteria for Susac syndrome.

Authors:  Ilka Kleffner; Jan Dörr; Marius Ringelstein; Catharina C Gross; Yvonne Böckenfeld; Wolfram Schwindt; Benedikt Sundermann; Hubertus Lohmann; Heike Wersching; Julia Promesberger; Natascha von Königsmarck; Anne Alex; Rainer Guthoff; Catharina J M Frijns; L Jaap Kappelle; Sven Jarius; Brigitte Wildemann; Orhan Aktas; Friedemann Paul; Heinz Wiendl; Thomas Duning
Journal:  J Neurol Neurosurg Psychiatry       Date:  2016-10-25       Impact factor: 10.154

Review 2.  Characteristics of Susac syndrome: a review of all reported cases.

Authors:  Jan Dörr; Sarah Krautwald; Brigitte Wildemann; Sven Jarius; Marius Ringelstein; Thomas Duning; Orhan Aktas; Erich Bernd Ringelstein; Friedemann Paul; Ilka Kleffner
Journal:  Nat Rev Neurol       Date:  2013-04-30       Impact factor: 42.937

3.  Susac Syndrome: A Rare Cause of a Confusional State.

Authors:  Chen Ben David; Kassem Sharif; Abdulla Watad; Nicola Luigi Bragazzi; Mohammad Adawi
Journal:  Isr Med Assoc J       Date:  2017-10       Impact factor: 0.892

4.  Guidelines for treatment of Susac syndrome - An update.

Authors:  Robert M Rennebohm; Negar Asdaghi; Sunil Srivastava; Elie Gertner
Journal:  Int J Stroke       Date:  2018-01-10       Impact factor: 5.266

5.  Susac's syndrome: the triad of microangiopathy of the brain and retina with hearing loss in young women.

Authors:  J O Susac
Journal:  Neurology       Date:  1994-04       Impact factor: 9.910

6.  Brain microvascular pathology in Susac syndrome: an electron microscopic study of five cases.

Authors:  Dimitri P Agamanolis; Richard A Prayson; Negar Asdaghi; Sakir H Gultekin; Kim Bigley; Robert M Rennebohm
Journal:  Ultrastruct Pathol       Date:  2019-11-16       Impact factor: 1.094

Review 7.  MRI findings in Susac's syndrome.

Authors:  J O Susac; F R Murtagh; R A Egan; J R Berger; R Bakshi; N Lincoff; A D Gean; S L Galetta; R J Fox; F E Costello; A G Lee; J Clark; R B Layzer; R B Daroff
Journal:  Neurology       Date:  2003-12-23       Impact factor: 9.910

8.  Clinical, paraclinical and serological findings in Susac syndrome: an international multicenter study.

Authors:  Sven Jarius; Ilka Kleffner; Jan M Dörr; Jaume Sastre-Garriga; Zsolt Illes; Eric Eggenberger; Colin Chalk; Marius Ringelstein; Orhan Aktas; Xavier Montalban; Kai Fechner; Winfried Stöcker; Erich B Ringelstein; Friedemann Paul; Brigitte Wildemann
Journal:  J Neuroinflammation       Date:  2014-03-08       Impact factor: 8.322

9.  Recurrence of Susac Syndrome following 23 Years of Remission.

Authors:  Amalia Feresiadou; Urban Eriksson; Hans-Christian Larsen; Raili Raininko; Ingela Nygren; Atle Melberg
Journal:  Case Rep Neurol       Date:  2014-05-21

10.  CD8+ T cell-mediated endotheliopathy is a targetable mechanism of neuro-inflammation in Susac syndrome.

Authors:  Catharina C Gross; Céline Meyer; Urvashi Bhatia; Lidia Yshii; Ilka Kleffner; Jan Bauer; Anna R Tröscher; Andreas Schulte-Mecklenbeck; Sebastian Herich; Tilman Schneider-Hohendorf; Henrike Plate; Tanja Kuhlmann; Markus Schwaninger; Wolfgang Brück; Marc Pawlitzki; David-Axel Laplaud; Delphine Loussouarn; John Parratt; Michael Barnett; Michael E Buckland; Todd A Hardy; Stephen W Reddel; Marius Ringelstein; Jan Dörr; Brigitte Wildemann; Markus Kraemer; Hans Lassmann; Romana Höftberger; Eduardo Beltrán; Klaus Dornmair; Nicholas Schwab; Luisa Klotz; Sven G Meuth; Guillaume Martin-Blondel; Heinz Wiendl; Roland Liblau
Journal:  Nat Commun       Date:  2019-12-18       Impact factor: 14.919

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