Kaposi Sarcoma of the Face Not Associated with Acquired Immunodeficiency Syndrome: A Case Report and Review of the Literature.

Kaposi sarcoma (KS) is an angioproliferative vascular neoplasm characterized by the proliferation of endothelial cells that is typically seen in patients with acquired immunodeficiency syndrome (AIDS). There are four major subtypes of KS: classic, African endemic, iatrogenic, and AIDS-associated KS. In rare circumstances, a patient might present with KS that does not fit into any of the four major subtypes and has no identifiable predisposing factors. This case report and review of the literature is presented to serve as a reminder to practitioners to suspect the unexpected when considering cystic or vascular-type lesions on the head and neck.