Literature DB >> 3472484

Targeting of nuclear-encoded proteins to the mitochondrial matrix: implications for human genetic defects.

L E Rosenberg, W A Fenton, A L Horwich, F Kalousek, J P Kraus.   

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Year:  1986        PMID： 3472484     DOI： 10.1111/j.1749-6632.1986.tb46550.x

Source DB:  PubMed          Journal:  Ann N Y Acad Sci        ISSN： 0077-8923            Impact factor:   5.691


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  9 in total

1.  Identification of RNA splicing errors resulting in human ornithine transcarbamylase deficiency.

Authors:  R P Carstens; W A Fenton; L R Rosenberg
Journal:  Am J Hum Genet       Date:  1991-06       Impact factor: 11.025

2.  Two mitochondrial matrix proteases act sequentially in the processing of mammalian matrix enzymes.

Authors:  F Kalousek; J P Hendrick; L E Rosenberg
Journal:  Proc Natl Acad Sci U S A       Date:  1988-10       Impact factor: 11.205

3.  Changes in brain mitochondrial bioenergetics in protein-deficient rats.

Authors:  O O Olorunsogo
Journal:  Br J Exp Pathol       Date:  1989-12

Review 4.  Molecular defects in cytochrome oxidase in mitochondrial diseases.

Authors:  S DiMauro; M Zeviani; R Rizzuto; A Lombes; H Nakase; E Bonilla; A Miranda; E Schon
Journal:  J Bioenerg Biomembr       Date:  1988-06       Impact factor: 2.945

5.  Mitochondrial import and processing of mutant human ornithine transcarbamylase precursors in cultured cells.

Authors:  G Isaya; W A Fenton; J P Hendrick; K Furtak; F Kalousek; L E Rosenberg
Journal:  Mol Cell Biol       Date:  1988-12       Impact factor: 4.272

6.  Cleavage of precursors by the mitochondrial processing peptidase requires a compatible mature protein or an intermediate octapeptide.

Authors:  G Isaya; F Kalousek; W A Fenton; L E Rosenberg
Journal:  J Cell Biol       Date:  1991-04       Impact factor: 10.539

7.  Rat liver mitochondrial intermediate peptidase (MIP): purification and initial characterization.

Authors:  F Kalousek; G Isaya; L E Rosenberg
Journal:  EMBO J       Date:  1992-08       Impact factor: 11.598

8.  An enzyme trafficking defect in two patients with primary hyperoxaluria type 1: peroxisomal alanine/glyoxylate aminotransferase rerouted to mitochondria.

Authors:  C J Danpure; P J Cooper; P J Wise; P R Jennings
Journal:  J Cell Biol       Date:  1989-04       Impact factor: 10.539

9.  Import of rat ornithine transcarbamylase precursor into mitochondria: two-step processing of the leader peptide.

Authors:  E S Sztul; J P Hendrick; J P Kraus; D Wall; F Kalousek; L E Rosenberg
Journal:  J Cell Biol       Date:  1987-12       Impact factor: 10.539
  9 in total

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