Literature DB >> 3464427

Impaired monocyte function in glycogen storage disease type Ib.

N Ueno, M Tomita, T Ariga, M Ohkawa, S Nagano, Y Takahashi, S Arashima, S Matsumoto.   

Abstract

Phagocyte (neutrophil and monocyte) function was evaluated in a boy with glycogen storage disease type Ib. Neutrophils were found to be defective in motility and respiratory burst and monocytes showed a defect in respiratory burst but not in motility. These results suggested that the glucose-6-phosphate transport system plays a role in the function of neutrophils and monocytes and that these two phagocytes are different from each other in their energy metabolism for motility.

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Year:  1986        PMID： 3464427     DOI： 10.1007/BF00439409

Source DB:  PubMed          Journal:  Eur J Pediatr        ISSN： 0340-6199            Impact factor:   3.183


  15 in total

1.  Type Ib glycogen storage disease is caused by a defect in the glucose-6-phosphate translocase of the microsomal glucose-6-phosphatase system.

Authors:  A J Lange; W J Arion; A L Beaudet
Journal:  J Biol Chem       Date:  1980-09-25       Impact factor: 5.157

2.  Neutropenia in a patient with type IB glycogen storage disease: in vitro response to lithium chloride.

Authors:  E R McCabe; T R Melvin; D O'Brien; R R Montgomery; W A Robinson; C Bhasker; B I Brown
Journal:  J Pediatr       Date:  1980-12       Impact factor: 4.406

Review 3.  Regulation of the immune response--role of the macrophage.

Authors:  A S Rosenthal
Journal:  N Engl J Med       Date:  1980-11-13       Impact factor: 91.245

4.  The macrophage as an effector cell.

Authors:  C F Nathan; H W Murray; Z A Cohn
Journal:  N Engl J Med       Date:  1980-09-11       Impact factor: 91.245

5.  In vitro bactericidal capacity of human polymorphonuclear leukocytes: diminished activity in chronic granulomatous disease of childhood.

Authors:  P G Quie; J G White; B Holmes; R A Good
Journal:  J Clin Invest       Date:  1967-04       Impact factor: 14.808

6.  Impaired metabolic function of polymorphonuclear leukocytes in glycogen storage disease Ib.

Authors:  M Gahr; K Heyne
Journal:  Eur J Pediatr       Date:  1983-09       Impact factor: 3.183

7.  Short communication. Glycogenosis Ib: neutrophil microbicidal defects due to impaired hexose monophosphate shunt.

Authors:  R Seger; B Steinmann; L Tiefenauer; T Matsunaga; R Gitzelmann
Journal:  Pediatr Res       Date:  1984-03       Impact factor: 3.756

8.  Neutropenia and impaired neutrophil function in glycogenosis type Ib.

Authors:  M Di Rocco; C Borrone; F Dallegri; G Frumento; F Patrone
Journal:  J Inherit Metab Dis       Date:  1984       Impact factor: 4.982

9.  Infectious and bleeding complications in patients with glycogenosis Ib.

Authors:  D R Ambruso; E R McCabe; D Anderson; A Beaudet; L M Ballas; I K Brandt; B Brown; R Coleman; D B Dunger; J M Falletta
Journal:  Am J Dis Child       Date:  1985-07

Review 10.  Glycogen storage disease type Ib.

Authors:  J Schaub; K Heyne
Journal:  Eur J Pediatr       Date:  1983-09       Impact factor: 3.183
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  2 in total

1.  Impaired metabolic function and signaling defects in phagocytic cells in glycogen storage disease type 1b.

Authors:  L Kilpatrick; B Z Garty; K F Lundquist; K Hunter; C A Stanley; L Baker; S D Douglas; H M Korchak
Journal:  J Clin Invest       Date:  1990-07       Impact factor: 14.808

Review 2.  Glycogen storage diseases: new perspectives.

Authors:  Hasan Ozen
Journal:  World J Gastroenterol       Date:  2007-05-14       Impact factor: 5.742
  2 in total

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