| Literature DB >> 34546401 |
Britta Franziska Zecher1,2, Roman Zenouzi1, Melanie Lang3, Panagiotis Karagiannis4, Till Clauditz5, Lutz Fischer3,6, Martina Sterneck1,3, Christoph Schramm1,2,7, Ansgar W Lohse1,2, Marcial Sebode8,9.
Abstract
Langerhans cell histiocytosis (LCH) is a very rare cause of secondary sclerosing cholangitis. We report the case of a 42-year-old male patient with sclerosing cholangitis and histological evidence of LCH from a bile duct biopsy. Due to rapid disease progression and exhaustion of conservative therapeutic approaches the patient received a liver transplantation. Nearly 2 years after transplantation the patient has a good graft function and no signs of recurrence of the underlying LCH.Entities:
Keywords: Cholangiography, endoscopic retrograde; Cholangitis, sclerosing, secondary; Histiocytosis, Langerhans cell; Liver transplantation; Unclear cholestasis
Mesh:
Year: 2021 PMID: 34546401 DOI: 10.1007/s00108-021-01148-0
Source DB: PubMed Journal: Internist (Berl) ISSN: 0020-9554 Impact factor: 0.743