Literature DB >> 34265145

An exploration of why men with severe haemophilia might not want gene therapy: The exigency study.

Simon Fletcher1, Kathryn Jenner2, Michael Holland2, Steve Chaplin2, Kate Khair2.   

Abstract

INTRODUCTION: For many people with haemophilia (PwH) gene therapy offers a potential functional cure. However, some have stated that they do not wish to have gene therapy either now or in the future. AIM: This sub-study, part of the larger Exigency programme, assesses the attitudes, views and understanding of those who do not wish to undergo gene therapy.
METHODS: Participants were approached via social media and word of mouth referral and invited to participate in a focus group or individual interview to discuss their views. Interviews were recorded, transcribed verbatim and analysed thematically.
RESULTS: Ten adult men with severe haemophilia (eight haemophilia A and two haemophilia B), mean age 34.3 years, participated in a 1-h focus group (n = 9) or interview (n = 1). All were on prophylaxis. None reported significant treatment burden, and all had annual bleeding rates of less than five in the previous 12 months. Four major themes emerged: self-identity and its loss, lack of long-term safety and efficacy data, ongoing concerns about past viral infection, and lack of current treatment burden.
CONCLUSION: There are many concerns about gene therapy, including eligibility, effectiveness and safety, which may result in individuals declining it as a therapy. These concerns may recede as more data are published. This study reveals a psychological dynamic around self-identity and belonging for PwH. The nature of this dynamic is poorly understood and needs exploration to facilitate support for those making decisions about gene therapy.
© 2021 John Wiley & Sons Ltd.

Entities:  

Keywords:  decision making; gene therapy; haemophilia; informed consent; self-identity; treatment burden

Year:  2021        PMID: 34265145     DOI: 10.1111/hae.14378

Source DB:  PubMed          Journal:  Haemophilia        ISSN: 1351-8216            Impact factor:   4.287


  1 in total

1.  The experiences of people with haemophilia and their families of gene therapy in a clinical trial setting: regaining control, the Exigency study.

Authors:  Simon Fletcher; Kathryn Jenner; Luke Pembroke; Michael Holland; Kate Khair
Journal:  Orphanet J Rare Dis       Date:  2022-04-04       Impact factor: 4.123

  1 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.