Literature DB >> 34219945

Intestinal angioedema caused by an acquired C1 esterase inhibitor deficiency associated with underlying splenic marginal zone lymphoma.

Thanita Thongtan1, Anasua Deb1, Genanew Bedanie1, Mohamed Elmassry1, Matthew Soape1, Kenneth Nugent1.   

Abstract

A 75-year-old woman presented with recurrent abdominal pain and vomiting for 1 year and was later found to have splenomegaly and pancytopenia. This case report depicts a clinical picture of intestinal angioedema, a challenging diagnosis, and an underlying rare syndrome of acquired C1 esterase inhibitor deficiency associated with splenic marginal zone lymphoma.
Copyright © 2021 Baylor University Medical Center.

Entities:  

Keywords:  C1 esterase inhibitor deficiency; intestinal angioedema; splenic marginal zone lymphoma

Year:  2021        PMID: 34219945      PMCID: PMC8224193          DOI: 10.1080/08998280.2021.1885277

Source DB:  PubMed          Journal:  Proc (Bayl Univ Med Cent)        ISSN: 0899-8280


  7 in total

1.  Hereditary and acquired angioedema: problems and progress: proceedings of the third C1 esterase inhibitor deficiency workshop and beyond.

Authors:  Angelo Agostoni; Emel Aygören-Pürsün; Karen E Binkley; Alvaro Blanch; Konrad Bork; Laurence Bouillet; Christoph Bucher; Anthony J Castaldo; Marco Cicardi; Alvin E Davis; Caterina De Carolis; Christian Drouet; Christiane Duponchel; Henriette Farkas; Kálmán Fáy; Béla Fekete; Bettina Fischer; Luigi Fontana; George Füst; Roberto Giacomelli; Albrecht Gröner; C Erik Hack; George Harmat; John Jakenfelds; Mathias Juers; Lajos Kalmár; Pál N Kaposi; István Karádi; Arianna Kitzinger; Tímea Kollár; Wolfhart Kreuz; Peter Lakatos; Hilary J Longhurst; Margarita Lopez-Trascasa; Inmaculada Martinez-Saguer; Nicole Monnier; István Nagy; Eva Németh; Erik Waage Nielsen; Jan H Nuijens; Caroline O'grady; Emanuela Pappalardo; Vincenzo Penna; Carlo Perricone; Roberto Perricone; Ursula Rauch; Olga Roche; Eva Rusicke; Peter J Späth; George Szendei; Edit Takács; Attila Tordai; Lennart Truedsson; Lilian Varga; Beáta Visy; Kayla Williams; Andrea Zanichelli; Lorenza Zingale
Journal:  J Allergy Clin Immunol       Date:  2004-09       Impact factor: 10.793

Review 2.  Acquired deficiency of the inhibitor of the first complement component: presentation, diagnosis, course, and conventional management.

Authors:  Lorenza Chiara Zingale; Roberto Castelli; Andrea Zanichelli; Marco Cicardi
Journal:  Immunol Allergy Clin North Am       Date:  2006-11       Impact factor: 3.479

3.  High prevalence of splenic marginal zone lymphoma among patients with acquired C1 inhibitor deficiency.

Authors:  Roberto Castelli; Maddalena Alessandra Wu; Massimo Arquati; Andrea Zanichelli; Chiara Suffritti; Davide Rossi; Marco Cicardi
Journal:  Br J Haematol       Date:  2016-01-05       Impact factor: 6.998

4.  Classification, diagnosis, and approach to treatment for angioedema: consensus report from the Hereditary Angioedema International Working Group.

Authors:  M Cicardi; W Aberer; A Banerji; M Bas; J A Bernstein; K Bork; T Caballero; H Farkas; A Grumach; A P Kaplan; M A Riedl; M Triggiani; A Zanichelli; B Zuraw
Journal:  Allergy       Date:  2014-03-27       Impact factor: 13.146

5.  CT of angioedema of the small bowel.

Authors:  A I De Backer; A M De Schepper; J E Vandevenne; P Schoeters; P Michielsen; W J Stevens
Journal:  AJR Am J Roentgenol       Date:  2001-03       Impact factor: 3.959

Review 6.  Diagnosis and management of angioedema with abdominal involvement: a gastroenterology perspective.

Authors:  Ugochukwu C Nzeako
Journal:  World J Gastroenterol       Date:  2010-10-21       Impact factor: 5.742

Review 7.  Gastrointestinal manifestations, diagnosis, and management of hereditary angioedema.

Authors:  Sujai Jalaj; James S Scolapio
Journal:  J Clin Gastroenterol       Date:  2013 Nov-Dec       Impact factor: 3.062

  7 in total

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