| Literature DB >> 34165242 |
Hilary J Vernon1, Irini Manoli2.
Abstract
From Sir Archibald Garrod's initial description of the tetrad of albinism, alkaptonuria, cystinuria, and pentosuria to today, the field of medicine dedicated to inborn errors of metabolism has evolved from disease identification and mechanistic discovery to the development of therapies designed to subvert biochemical defects. In this review, we highlight major milestones in the treatment and diagnosis of inborn errors of metabolism, starting with dietary therapy for phenylketonuria in the 1950s and 1960s, and ending with current approaches in genetic manipulation.Entities:
Keywords: enzyme replacement therapy; gene therapy; inborn errors of metabolism; substrate therapy
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Year: 2021 PMID: 34165242 DOI: 10.1002/ajmg.a.62385
Source DB: PubMed Journal: Am J Med Genet A ISSN: 1552-4825 Impact factor: 2.802