A Rare Case of Exocrine Pancreatic Insufficiency.

Lipomatous pseudohypertrophy (LPH) of the pancreas is an uncommon affection of exocrine pancreatic insufficiency. It is defined as substitution of the pancreatic exocrine gland by a large fat component. We report the case of a young patient with malabsorption syndrome (chronic diarrhoea and steatorrhoea), abnormal laboratory results and normal fibroscopy. Computed tomography revealed characteristic diffuse pancreatic abnormalities. LEARNING POINTS: Computed tomography is key for identifying lipomatous pseudohypertrophy.Malabsorption syndrome is usually associated with lipomatous pseudohypertrophy.A syndromic aetiology should be considered. © EFIM 2021.