Literature DB >> 33953480

Rapidly progressive fatal hypoxia in a young woman.

Aaron J Sohn1, Joseph M Guileyardo1, Alastair J Moore2, Kenneth A Ausloos3, Chetan A Naik3.   

Abstract

We present a rare cause of pulmonary arterial hypertension in a 29-year-old woman with rapidly progressive and fatal hypoxia. Subsequent workup revealed classic radiological findings and pathologic confirmation of pulmonary veno-occlusive disease.
Copyright © 2021 Baylor University Medical Center.

Entities:  

Keywords:  Pulmonary arterial hypertension; pulmonary hypertension; pulmonary veno-occlusive disease

Year:  2021        PMID: 33953480      PMCID: PMC8059900          DOI: 10.1080/08998280.2020.1871279

Source DB:  PubMed          Journal:  Proc (Bayl Univ Med Cent)        ISSN: 0899-8280


  9 in total

Review 1.  Pulmonary veno-occlusive disease.

Authors:  D Montani; L C Price; P Dorfmuller; L Achouh; X Jaïs; A Yaïci; O Sitbon; D Musset; G Simonneau; M Humbert
Journal:  Eur Respir J       Date:  2009-01       Impact factor: 16.671

2.  Beyond arterial remodelling: pulmonary venous and cardiac involvement in patients with systemic sclerosis-associated pulmonary arterial hypertension.

Authors:  P Dorfmüller; D Montani; M Humbert
Journal:  Eur Respir J       Date:  2010-01       Impact factor: 16.671

Review 3.  Chemotherapy-induced pulmonary hypertension: role of alkylating agents.

Authors:  Benoît Ranchoux; Sven Günther; Rozenn Quarck; Marie-Camille Chaumais; Peter Dorfmüller; Fabrice Antigny; Sébastien J Dumas; Nicolas Raymond; Edmund Lau; Laurent Savale; Xavier Jaïs; Olivier Sitbon; Gérald Simonneau; Kurt Stenmark; Sylvia Cohen-Kaminsky; Marc Humbert; David Montani; Frédéric Perros
Journal:  Am J Pathol       Date:  2014-12-11       Impact factor: 4.307

4.  Pulmonary veno-occlusive disease: a case series and new observations.

Authors:  B W Holcomb; J E Loyd; E W Ely; J Johnson; I M Robbins
Journal:  Chest       Date:  2000-12       Impact factor: 9.410

5.  [Pulmonary veno-occlusive disease in a patient with HIV infection. A case report with autopsy findings].

Authors:  Muriel Hourseau; Frédérique Capron; Hilario Nunes; Pascal Godmer; Antoine Martin; Marianne Kambouchner
Journal:  Ann Pathol       Date:  2002-12       Impact factor: 0.407

6.  EIF2AK4 mutations cause pulmonary veno-occlusive disease, a recessive form of pulmonary hypertension.

Authors:  Mélanie Eyries; David Montani; Barbara Girerd; Claire Perret; Anne Leroy; Christine Lonjou; Nadjim Chelghoum; Florence Coulet; Damien Bonnet; Peter Dorfmüller; Elie Fadel; Olivier Sitbon; Gérald Simonneau; David-Alexandre Tregouët; Marc Humbert; Florent Soubrier
Journal:  Nat Genet       Date:  2013-12-01       Impact factor: 38.330

Review 7.  Pathologic assessment of vasculopathies in pulmonary hypertension.

Authors:  Giuseppe G Pietra; Frederique Capron; Susan Stewart; Ornella Leone; Marc Humbert; Ivan M Robbins; Lynne M Reid; R M Tuder
Journal:  J Am Coll Cardiol       Date:  2004-06-16       Impact factor: 24.094

8.  Pulmonary veno-occlusive disease: clinical, functional, radiologic, and hemodynamic characteristics and outcome of 24 cases confirmed by histology.

Authors:  David Montani; Lara Achouh; Peter Dorfmüller; Jérôme Le Pavec; Benjamin Sztrymf; Colas Tchérakian; Anne Rabiller; Rehan Haque; Olivier Sitbon; Xavier Jaïs; Philippe Dartevelle; Sophie Maître; Frédérique Capron; Dominique Musset; Gérald Simonneau; Marc Humbert
Journal:  Medicine (Baltimore)       Date:  2008-07       Impact factor: 1.889

9.  Occupational exposure to organic solvents: a risk factor for pulmonary veno-occlusive disease.

Authors:  David Montani; Edmund M Lau; Alexis Descatha; Xavier Jaïs; Laurent Savale; Pascal Andujar; Lynda Bensefa-Colas; Barbara Girerd; Inès Zendah; Jerome Le Pavec; Andrei Seferian; Frédéric Perros; Peter Dorfmüller; Elie Fadel; Florent Soubrier; Oliver Sitbon; Gérald Simonneau; Marc Humbert
Journal:  Eur Respir J       Date:  2015-11-05       Impact factor: 16.671

  9 in total

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