Ira Goldsmith1, Joseph George2, Umair Aslam2, Sobaran Sharma2. 1. Department of Cardiothoracic Surgery, Swansea Bay University Health Board, Morriston Hospital, Swansea, Wales, SA6 6NL, UK. ira.goldsmith@wales.nhs.uk. 2. Department of Cardiothoracic Surgery, Swansea Bay University Health Board, Morriston Hospital, Swansea, Wales, SA6 6NL, UK.
Abstract
BACKGROUND: Congenital pulmonary airway malformation (CPAM) with partial anomalous pulmonary venous connection presenting as episodic retrosternal chest pain on exertion in an adult has not been described. CASE PRESENTATION: A 21-year-old female, non-smoker, presented with a 4-year history of sharp, episodic, retrosternal chest pains brought on with exercise. A contrast-enhanced computed tomography (CT) scan showed a grossly overinflated left lower lobe with partial anomalous pulmonary venous drainage into the left hemi-azygos vein. Lobectomy, the recommended treatment of choice, carried out thoracoscopically, was curative with satisfactory mid-term results. Histology confirmed type-II congenital pulmonary airway malformation. CONCLUSIONS: CPAM can present in young adults with unusual symptoms of chest pain on exertion. When suspected a contrast-enhanced CT scan is the gold standard for establishing the diagnosis. An anatomical lung resection is curative with satisfactory medium term results.
BACKGROUND:Congenital pulmonary airway malformation (CPAM) with partial anomalous pulmonary venous connection presenting as episodic retrosternal chest pain on exertion in an adult has not been described. CASE PRESENTATION: A 21-year-old female, non-smoker, presented with a 4-year history of sharp, episodic, retrosternal chest pains brought on with exercise. A contrast-enhanced computed tomography (CT) scan showed a grossly overinflated left lower lobe with partial anomalous pulmonary venous drainage into the left hemi-azygos vein. Lobectomy, the recommended treatment of choice, carried out thoracoscopically, was curative with satisfactory mid-term results. Histology confirmed type-II congenital pulmonary airway malformation. CONCLUSIONS: CPAM can present in young adults with unusual symptoms of chest pain on exertion. When suspected a contrast-enhanced CT scan is the gold standard for establishing the diagnosis. An anatomical lung resection is curative with satisfactory medium term results.
Authors: J M Laberge; H Flageole; D Pugash; S Khalife; G Blair; D Filiatrault; P Russo; G Lees; R D Wilson Journal: Fetal Diagn Ther Date: 2001 May-Jun Impact factor: 2.587
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