| Literature DB >> 33827121 |
Saori Taharabaru1,2, Takehito Sato1, Kimitoshi Nishiwaki1.
Abstract
Nicolaides-Baraitser syndrome (NCBRS) is a rare congenital genetic disorder characterized by distinctive facial features similar to Treacher Collins syndrome (TCS). We report the first case of successful nasal fiberoptic intubation in a patient with NCBRS with micrognathia and limited mouth opening due to trismus. A 9-year-old girl with NCBRS and dental caries was scheduled to undergo general anesthesia for a dental extraction. Initial attempts at oral intubation using a video laryngoscope were unsuccessful. However, subsequent attempts at nasal intubation using a flexible fiberoptic scope were successful. This report highlights that patients with NCBRS may present with difficult airways to manage and intubate.Entities:
Keywords: Difficult airway; Fiberoptic intubation; Nicolaides-Baraitser syndrome; Pediatric anesthesia
Year: 2021 PMID: 33827121 PMCID: PMC8033586 DOI: 10.2344/anpr-67-04-05
Source DB: PubMed Journal: Anesth Prog ISSN: 0003-3006