Literature DB >> 33827121

Difficult Airway Management in a Patient With Nicolaides-Baraitser Syndrome Who Had a Small Jaw and Limited Mouth Opening.

Saori Taharabaru1,2, Takehito Sato1, Kimitoshi Nishiwaki1.   

Abstract

Nicolaides-Baraitser syndrome (NCBRS) is a rare congenital genetic disorder characterized by distinctive facial features similar to Treacher Collins syndrome (TCS). We report the first case of successful nasal fiberoptic intubation in a patient with NCBRS with micrognathia and limited mouth opening due to trismus. A 9-year-old girl with NCBRS and dental caries was scheduled to undergo general anesthesia for a dental extraction. Initial attempts at oral intubation using a video laryngoscope were unsuccessful. However, subsequent attempts at nasal intubation using a flexible fiberoptic scope were successful. This report highlights that patients with NCBRS may present with difficult airways to manage and intubate.
© 2021 by the American Dental Society of Anesthesiology.

Entities:  

Keywords:  Difficult airway; Fiberoptic intubation; Nicolaides-Baraitser syndrome; Pediatric anesthesia

Year:  2021        PMID: 33827121      PMCID: PMC8033586          DOI: 10.2344/anpr-67-04-05

Source DB:  PubMed          Journal:  Anesth Prog        ISSN: 0003-3006


  2 in total

1.  The change of difficult intubation with growth in a patient with treacher Collins syndrome.

Authors:  Gaku Inagawa; Takaaki Miwa; Koichi Hiroki
Journal:  Anesth Analg       Date:  2004-12       Impact factor: 5.108

2.  Congenital mandibular hypoplasia: analysis and classification.

Authors:  Davinder J Singh; Scott P Bartlett
Journal:  J Craniofac Surg       Date:  2005-03       Impact factor: 1.046

  2 in total
  1 in total

1.  Anaesthesia and orphan disease: management of a case of Nicolaides-Baraitser syndrome undergoing cleft palate surgery.

Authors:  Marie Goehring; Suma Choorapoikayil; Kai Zacharowski; Leila Messroghli
Journal:  BMC Anesthesiol       Date:  2021-05-26       Impact factor: 2.217

  1 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.