Literature DB >> 33750365

Multiple odontogenic keratocysts in Ehlers-Danlos syndrome: a rare case report.

Anna Starzyńska1, Paulina Adamska2, Łukasz Adamski2, Aleksandra Sejda3, Piotr Wychowański4, Michał Studniarek5, Barbara Alicja Jereczek-Fossa6,7.   

Abstract

BACKGROUND: An odontogenic keratocyst is a lesion characterized by aggressive and infiltrative growth. The lesion is characterized by the existence of satellite microcysts (microtumours) and frequent recurrence (up to 30%). Ehlers-Danlos syndrome is a condition in which collagen production or its post-translational modifications are affected. Defects in connective tissues cause symptoms, which range from mild joint hypermobility to life-threatening complications. CASE
PRESENTATION: We present an extremely rare case of an 11-year old girl with Ehlers-Danlos syndrome and coexistence of multiple odontogenic keratocysts.
CONCLUSIONS: This case shows mainly atypical or rare association between multiple odontogenic keratocysts and Ehlers-Danlos syndrome.

Entities:  

Keywords:  Case report; Dentigerous cyst; Ehlers–Danlos syndrome; Odontogenic keratocysts; Paediatric dentistry

Year:  2021        PMID： 33750365      PMCID： PMC7941700          DOI： 10.1186/s12903-021-01472-9

Source DB:  PubMed          Journal:  BMC Oral Health        ISSN： 1472-6831            Impact factor:   2.757


  28 in total

1.  Temporomandibular joint problems and self-registration of mandibular opening capacity among adults with Ehlers-Danlos syndrome. A questionnaire study.

Authors:  Catharina Hagberg; Lena Korpe; Britta Berglund
Journal:  Orthod Craniofac Res       Date:  2004-02       Impact factor: 1.826

Review 2.  Hypermobile Ehlers-Danlos syndrome (a.k.a. Ehlers-Danlos syndrome Type III and Ehlers-Danlos syndrome hypermobility type): Clinical description and natural history.

Authors:  Brad Tinkle; Marco Castori; Britta Berglund; Helen Cohen; Rodney Grahame; Hanadi Kazkaz; Howard Levy
Journal:  Am J Med Genet C Semin Med Genet       Date:  2017-02-01       Impact factor: 3.908

3.  Clinical utility gene card for: Ehlers-Danlos syndrome types I-VII and variants - update 2012.

Authors:  Karin Mayer; Ingo Kennerknecht; Beat Steinmann
Journal:  Eur J Hum Genet       Date:  2012-08-15       Impact factor: 4.246

4.  The natural history, including orofacial features of three patients with Ehlers-Danlos syndrome, dermatosparaxis type (EDS type VIIC).

Authors:  Fransiska Malfait; Peter De Coster; Ingrid Hausser; Anthonie J van Essen; Peter Franck; Alain Colige; Betty Nusgens; Luc Martens; Anne De Paepe
Journal:  Am J Med Genet A       Date:  2004-11-15       Impact factor: 2.802

Review 5.  Keratocystic Odontogenic Tumours: Etiology, Pathogenesis and Treatment Revisited.

Authors:  Suresh Menon
Journal:  J Maxillofac Oral Surg       Date:  2014-12-16

Review 6.  Odontogenic keratocyst and multiple supernumerary teeth in a patient with Ehlers-Danlos syndrome--a case report and review of the literature.

Authors:  Osny Ferreira; Camila Lopes Cardoso; Ana Lúcia Alvares Capelozza; Renato Yassutaka Faria Yaedú; Antõnio Richieri da Costa
Journal:  Quintessence Int       Date:  2008-03       Impact factor: 1.677

Review 7.  Multiple odontogenic keratocysts in a patient with type II (mitis) Ehlers-Danlos syndrome.

Authors:  R J Carr; D M Green
Journal:  Br J Oral Maxillofac Surg       Date:  1988-06       Impact factor: 1.651

8.  Women with Ehlers-Danlos syndrome experience low oral health-related quality of life.

Authors:  Britta Berglund; Erik Björck
Journal:  J Orofac Pain       Date:  2012

9.  Comparative analysis of the immunohistochemical expression of vascular endothelial growth factor and matrix metalloproteinase-9 in keratocystic odontogenic tumor, dentigerous cyst and radicular cyst.

Authors:  Komal Khot; Siddharth B Deshmukh; Sheeba Alex
Journal:  J Cancer Res Ther       Date:  2015 Jul-Sep       Impact factor: 1.805

Review 10.  What surgical treatment has the lowest recurrence rate following the management of keratocystic odontogenic tumor?: A large systematic review and meta-analysis.

Authors:  Essam Ahmed Al-Moraissi; Ayed Ali Dahan; Mohamed Salah Alwadeai; Fadekemi Olufunmilayo Oginni; Jamil Mohammed Al-Jamali; Ahmed Saleh Alkhutari; Nashwan Hamid Al-Tairi; Abdulrazaq Ahmed Almaweri; Jaber Saleh Al-Sanabani
Journal:  J Craniomaxillofac Surg       Date:  2016-10-31       Impact factor: 2.078
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