A Triki1,2, M Aloui3,4, M Ghalleb1,2, I Jbir1,2, Ben Naceur5,2, J Ben Hassouna1,2, R Chargui1,2, K Rahal1,2. 1. Surgical Oncology Department, Salah Azaiez Institute of Oncology, Tunis, Tunisia. 2. Faculty of Medicine, Tunis, Tunisia. 3. Surgical Oncology Department, Salah Azaiez Institute of Oncology, Tunis, Tunisia. marwaaloui10@gmail.com. 4. Faculty of Medicine, Tunis, Tunisia. marwaaloui10@gmail.com. 5. Plastic Surgery Unit, Salah Azaiez Institute of Oncology, Tunis, Tunisia.
Abstract
BACKGROUND: Darier-Ferrand dermatofibrosarcoma (DFS) is a rare malignant cutaneous neoplasm characterized by local aggressiveness, high risk of recurrence, and low metastatic potential. CASE PRESENTATION: A 60-year-old Tunisian man with recurrent abdominopelvic DFS for which he had undergone multiple excisions presented with an extensive DFS that invaded the external genitals. He underwent a large excision with emasculation and thin cutaneous graft of the abdominal wall and local skin flap in the pelvis. CONCLUSION: DFS is a rare yet recurrent skin tumor. Wide excision with free margins remains the cornerstone of treatment. We report a case of a giant DFS treated with wide excision and reconstructive surgery to cover the defect.
BACKGROUND: Darier-Ferrand dermatofibrosarcoma (DFS) is a rare malignant cutaneous neoplasm characterized by local aggressiveness, high risk of recurrence, and low metastatic potential. CASE PRESENTATION: A 60-year-old Tunisian man with recurrent abdominopelvic DFS for which he had undergone multiple excisions presented with an extensive DFS that invaded the external genitals. He underwent a large excision with emasculation and thin cutaneous graft of the abdominal wall and local skin flap in the pelvis. CONCLUSION: DFS is a rare yet recurrent skin tumor. Wide excision with free margins remains the cornerstone of treatment. We report a case of a giant DFS treated with wide excision and reconstructive surgery to cover the defect.
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