| Literature DB >> 33684494 |
Carmen M Montagnon1, Julia S Lehman2, Dedee F Murrell3, Michael J Camilleri2, Stanislav N Tolkachjov4.
Abstract
Subepidermal (subepithelial) autoimmune blistering dermatoses are a group of rare skin disorders characterized by the disruption of the dermal-epidermal junction through the action of autoantibodies. The fourth article in this continuing medical education series presents the current validated disease activity scoring systems, serologic parameters, treatments, and clinical trials for bullous pemphigoid, mucous membrane pemphigoid, epidermolysis bullosa acquisita, bullous systemic lupus erythematosus, anti-p200 pemphigoid, linear IgA bullous dermatosis, and dermatitis herpetiformis.Entities:
Keywords: anti-p200 pemphigoid; autoimmune blistering disease severity index system; autoimmune bullous disease quality of life; bullous pemphigoid; bullous pemphigoid disease area index; bullous systemic lupus erythematosus; dapsone; dermatitis herpetiformis; epidermolysis bullosa acquisita; linear IgA bullous dermatosis; mucous membrane pemphigoid; subepithelial autoimmune bullous dermatoses
Year: 2021 PMID: 33684494 DOI: 10.1016/j.jaad.2020.05.161
Source DB: PubMed Journal: J Am Acad Dermatol ISSN: 0190-9622 Impact factor: 11.527