| Literature DB >> 33669654 |
Ilaria Andreana1,2, Mathieu Repellin1,3, Flavia Carton3,4, David Kryza1,5, Stéphanie Briançon1, Bénédicte Chazaud6, Rémi Mounier6, Silvia Arpicco2, Manuela Malatesta3, Barbara Stella2, Giovanna Lollo1.
Abstract
Muscular Dystrophies (MDs) are a group of rare inherited genetic muscular pathologies encompassing a variety of clinical phenotypes, gene mutations and mechanisms of disease. MDs undergo progressive skeletal muscle degeneration causing severe health problems that lead to poor life quality, disability and premature death. There are no available therapies to counteract the causes of these diseases and conventional treatments are administered only to mitigate symptoms. Recent understanding on the pathogenetic mechanisms allowed the development of novel therapeutic strategies based on gene therapy, genome editing CRISPR/Cas9 and drug repurposing approaches. Despite the therapeutic potential of these treatments, once the actives are administered, their instability, susceptibility to degradation and toxicity limit their applications. In this frame, the design of delivery strategies based on nanomedicines holds great promise for MD treatments. This review focuses on nanomedicine approaches able to encapsulate therapeutic agents such as small chemical molecules and oligonucleotides to target the most common MDs such as Duchenne Muscular Dystrophy and the Myotonic Dystrophies. The challenge related to in vitro and in vivo testing of nanosystems in appropriate animal models is also addressed. Finally, the most promising nanomedicine-based strategies are highlighted and a critical view in future developments of nanomedicine for neuromuscular diseases is provided.Entities:
Keywords: CRISPR/Cas9; Duchenne Muscular Dystrophy; antisense oligonucleotides; myotonic dystrophy; nanoparticles; small molecules
Year: 2021 PMID: 33669654 DOI: 10.3390/pharmaceutics13020278
Source DB: PubMed Journal: Pharmaceutics ISSN: 1999-4923 Impact factor: 6.321