Literature DB >> 33645285

Isolated brachial artery aneurysm: a rare presentation of paediatric Behçet's disease.

A L Naik1, A Savlania1, A Gupta2, P Rastogi3, A Singh1.   

Abstract

Behçet's disease is a rare disease characterised by recurrent oral ulcers, with systemic manifestations including genital ulcers, ocular disease, skin lesions, gastrointestinal disease, neurologic disease, vascular disease and arthritis. Most clinical manifestations of Behçet's disease are believed to be due to vasculitis. The heterogeneous clinical spectrum is influenced by sex, ethnicity and country of residence. Vascular manifestation in the form of isolated large brachial artery aneurysm is rare in children. Treatment involves aneurysmorrhaphy to avoid rupture or ischaemic sequelae in addition to lifelong medical management to control vasculitis.

Entities:  

Keywords:  Behçet’s disease; Brachial artery aneurysm; Paediatric Behçet’s disease; Vascular Behçet’s disease

Mesh:

Substances:

Year:  2021        PMID: 33645285      PMCID: PMC9158231          DOI: 10.1308/rcsann.2020.7037

Source DB:  PubMed          Journal:  Ann R Coll Surg Engl        ISSN: 0035-8843            Impact factor:   1.951


  8 in total

1.  Behçet's disease, the Silk Road and HLA-B51: historical and geographical perspectives.

Authors:  D H Verity; J E Marr; S Ohno; G R Wallace; M R Stanford
Journal:  Tissue Antigens       Date:  1999-09

2.  Familial aggregation in Behçet's disease: high frequency in siblings and parents of pediatric probands.

Authors:  I Koné-Paut; I Geisler; B Wechsler; S Ozen; H Ozdogan; M Rozenbaum; I Touitou
Journal:  J Pediatr       Date:  1999-07       Impact factor: 4.406

Review 3.  Pediatric Behçet's disease - clinical aspects and current concepts.

Authors:  Mehmet Yıldız; Oya Köker; Amra Adrovic; Sezgin Şahin; Kenan Barut; Özgür Kasapçopur
Journal:  Eur J Rheumatol       Date:  2019-09-05

4.  Consensus classification criteria for paediatric Behçet's disease from a prospective observational cohort: PEDBD.

Authors:  Isabelle Koné-Paut; Fahrad Shahram; Martha Darce-Bello; Luca Cantarini; Rolando Cimaz; Marco Gattorno; Jordi Anton; Michael Hofer; Bouchra Chkirate; Kenza Bouayed; Ilknur Tugal-Tutkun; Jasmin Kuemmerle-Deschner; Hélène Agostini; Sylvia Federici; Armelle Arnoux; Celine Piedvache; Seza Ozen
Journal:  Ann Rheum Dis       Date:  2015-12-23       Impact factor: 19.103

5.  Genome-wide association study identifies variants in the MHC class I, IL10, and IL23R-IL12RB2 regions associated with Behçet's disease.

Authors:  Elaine F Remmers; Fulya Cosan; Yohei Kirino; Michael J Ombrello; Neslihan Abaci; Colleen Satorius; Julie M Le; Barbara Yang; Benjamin D Korman; Aris Cakiris; Oznur Aglar; Zeliha Emrence; Hulya Azakli; Duran Ustek; Ilknur Tugal-Tutkun; Gulsen Akman-Demir; Wei Chen; Christopher I Amos; Michael B Dizon; Afet Akdag Kose; Gulsevim Azizlerli; Burak Erer; Oliver J Brand; Virginia G Kaklamani; Phaedon Kaklamanis; Eldad Ben-Chetrit; Miles Stanford; Farida Fortune; Marwen Ghabra; William E R Ollier; Young-Hun Cho; Dongsik Bang; John O'Shea; Graham R Wallace; Massimo Gadina; Daniel L Kastner; Ahmet Gül
Journal:  Nat Genet       Date:  2010-07-11       Impact factor: 38.330

6.  Demographic and clinical properties of juvenile-onset Behçet's disease: A controlled multicenter study.

Authors:  Yelda Karincaoglu; Murat Borlu; Semra Cikman Toker; Ayse Akman; Meltem Onder; Suhan Gunasti; Aysegul Usta; Basak Kandi; Cicek Durusoy; Muammer Seyhan; Serap Utas; Hayriye Saricaoglu; Muge Guler Ozden; Soner Uzun; Umit Tursen; Demet Cicek; Levent Donmez; Erkan Alpsoy
Journal:  J Am Acad Dermatol       Date:  2007-11-28       Impact factor: 11.527

7.  2012 revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides.

Authors:  J C Jennette; R J Falk; P A Bacon; N Basu; M C Cid; F Ferrario; L F Flores-Suarez; W L Gross; L Guillevin; E C Hagen; G S Hoffman; D R Jayne; C G M Kallenberg; P Lamprecht; C A Langford; R A Luqmani; A D Mahr; E L Matteson; P A Merkel; S Ozen; C D Pusey; N Rasmussen; A J Rees; D G I Scott; U Specks; J H Stone; K Takahashi; R A Watts
Journal:  Arthritis Rheum       Date:  2013-01

8.  A national cohort study on pediatric Behçet's disease: cross-sectional data from an Italian registry.

Authors:  Romina Gallizzi; Caterina Pidone; Luca Cantarini; Martina Finetti; Marco Cattalini; Giovanni Filocamo; Antonella Insalaco; Donato Rigante; Rita Consolini; Maria Cristina Maggio; Adele Civino; Silvana Martino; Alma Nunzia Olivieri; Giovanna Fabio; Serena Pastore; Angela Mauro; Diana Sutera; Giuseppe Trimarchi; Nicolino Ruperto; Marco Gattorno; Rolando Cimaz
Journal:  Pediatr Rheumatol Online J       Date:  2017-12-21       Impact factor: 3.054

  8 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.