Literature DB >> 33552794

Tuberous Sclerosis: A Case Report and Review of the Literature.

Klenam Dzefi-Tettey1, Emmanuel K Edzie2, Philip Gorleku2, Albert D Piersson3, Obed Cudjoe4.   

Abstract

Tuberous sclerosis (TS) is a rare genetic disorder of autosomal-dominant inheritance. Mutations on either of the two genes Tuberous Sclerosis Complex 1 (TSC1) or Tuberous Sclerosis Complex 2 (TSC2) play a role and result in hamartomas involving many organs, like the brain, heart, kidneys, skin, lungs, and liver. This case report is about a four-year-old boy with facial angiofibromas, hypo-pigmented skin lesions on the lower back and dorsum of the right wrist, and previous history of seizures who was referred to the radiology department of the Korle Bu Teaching Hospital for Magnetic Resonance Imaging (MRI) of the brain. The MRI of the brain revealed subependymal giant cell astrocytomas, subependymal nodules, and cortical tubers. Ultrasonography of the abdomen also showed multiple angiomyolipomas and multiple simple cysts in both kidneys. The aim of this case report is to present the imaging findings and create awareness that this rare genetic disorder does exist in Ghana and advocate for formation of support groups for parents with children with tuberous sclerosis.
Copyright © 2021, Dzefi-Tettey et al.

Entities:  

Keywords:  angiofibromas; renal angiomyolipomas; seizures; subependymal giant cell astrocytoma; tuberous sclerosis

Year:  2021        PMID: 33552794      PMCID: PMC7854338          DOI: 10.7759/cureus.12481

Source DB:  PubMed          Journal:  Cureus        ISSN: 2168-8184


  14 in total

1.  Bilateral and multiple periungual fibromas as an oligosymptomatic form of tuberous sclerosis.

Authors:  Ricardo Ruiz-Villaverde; Jose Blasco-Melguizo; Isabel Hernández-Jurado; Ramón Naranjo-Sintes; M Teresa Gutierrez Salmerón
Journal:  Dermatology       Date:  2004       Impact factor: 5.366

2.  Shave and phenolization of periungual fibromas, Koenen's tumors, in a patient with tuberous sclerosis.

Authors:  Marta Mazaira; Jesús del Pozo Losada; Beatriz Fernández-Jorge; Rosa Fernández-Torres; Walter Martínez; Eduardo Fonseca
Journal:  Dermatol Surg       Date:  2007-12-05       Impact factor: 3.398

Review 3.  Tuberous sclerosis complex: Recent advances in manifestations and therapy.

Authors:  Mari Wataya-Kaneda; Motohide Uemura; Kazutoshi Fujita; Haruhiko Hirata; Keigo Osuga; Kuriko Kagitani-Shimono; Norio Nonomura
Journal:  Int J Urol       Date:  2017-07-01       Impact factor: 3.369

Review 4.  Tuberous sclerosis.

Authors:  P Curatolo; B L Maria
Journal:  Handb Clin Neurol       Date:  2013

Review 5.  Tuberous sclerosis complex: genetics to pathogenesis.

Authors:  Vinodh Narayanan
Journal:  Pediatr Neurol       Date:  2003-11       Impact factor: 3.372

Review 6.  Tuberous sclerosis complex consensus conference: revised clinical diagnostic criteria.

Authors:  E S Roach; M R Gomez; H Northrup
Journal:  J Child Neurol       Date:  1998-12       Impact factor: 1.987

Review 7.  The TSC1-TSC2 complex: a molecular switchboard controlling cell growth.

Authors:  Jingxiang Huang; Brendan D Manning
Journal:  Biochem J       Date:  2008-06-01       Impact factor: 3.857

Review 8.  Pictorial review of tuberous sclerosis in various organs.

Authors:  Shigeaki Umeoka; Takashi Koyama; Yukio Miki; Mikio Akai; Kazushige Tsutsui; Kaori Togashi
Journal:  Radiographics       Date:  2008-09-04       Impact factor: 5.333

Review 9.  Tuberous sclerosis.

Authors:  Paolo Curatolo; Roberta Bombardieri; Sergiusz Jozwiak
Journal:  Lancet       Date:  2008-08-23       Impact factor: 79.321

Review 10.  Tuberous sclerosis complex: advances in diagnosis, genetics, and management.

Authors:  Robert A Schwartz; Geover Fernández; Katarzyna Kotulska; Sergiusz Jóźwiak
Journal:  J Am Acad Dermatol       Date:  2007-08       Impact factor: 11.527

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  1 in total

1.  Congenital cardiac masses: a case report.

Authors:  Mohammed Alsabri; Alejandro Gonzalez; Aaron Sircy; Sai Sarada Policherla; Kemi Mascoll-Robertson
Journal:  J Med Case Rep       Date:  2022-04-22
  1 in total

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