Literature DB >> 33546345

Stem Cell Ophthalmology Treatment Study (SCOTS): Bone Marrow-Derived Stem Cells in the Treatment of Stargardt Disease.

Jeffrey N Weiss1, Steven Levy2.   

Abstract

Background: Stargardt Disease is the most common inherited macular degeneration, typically resulting in progressive central vision loss and legal blindness at an early age. We report regarding 34 eyes with Stargardt Disease treated in the Stem Cell Ophthalmology Treatment Study (SCOTS and SCOTS2).
Methods: Autologous bone marrow was processed, separating the stem cell fraction which was provided Arms using retrobulbar, subtenons, intravitreal or subretinal and intravenous. The follow-up period was one year.
Results: Of the 34 treated eyes, 21 (61.8%) improved, 8 (23.5%) remained stable, and 5 (14.7%) showed continued progression of their disease. Results were statistically significant with p = 0.0004. The average central vision improvement following treatment was 17.96% (95%CI, 16.39-19.53%) and ranged up to 80.5%. Of 17 patients treated, 13 (76.5%) showed visual acuity improvement in one or both eyes, 3 patients (17.6%) showed no net loss, and 1 worsened as a consequence of disease progression; 94.1% of patients had improved vision or remained stable. There were no adverse events. Conclusions: Patients with Stargardt Disease may potentially benefit from autologous bone marrow-derived stem cells (BMSC) as provided in SCOTS. Improvement or stabilization of vision was found to occur for the vast majority of reported patients and findings were highly statistically significant.

Entities:  

Keywords:  ABCA4 mutation; BMSC; SGDT1; Stargardt Disease; bone marrow-derived stem cells; hereditary macular degeneration; hereditary maculopathy; juvenile macular degeneration; macular degeneration; stem cells

Year:  2021        PMID: 33546345      PMCID: PMC7913552          DOI: 10.3390/medicines8020010

Source DB:  PubMed          Journal:  Medicines (Basel)        ISSN: 2305-6320


  20 in total

1.  Dual AAV Vectors for Stargardt Disease.

Authors:  Ivana Trapani
Journal:  Methods Mol Biol       Date:  2018

Review 2.  The Role of Gene Therapy in the Treatment of Retinal Diseases: A Review.

Authors:  C Campa; C E Gallenga; E Bolletta; P Perri
Journal:  Curr Gene Ther       Date:  2017       Impact factor: 4.391

3.  Human embryonic stem cell-derived retinal pigment epithelium in patients with age-related macular degeneration and Stargardt's macular dystrophy: follow-up of two open-label phase 1/2 studies.

Authors:  Steven D Schwartz; Carl D Regillo; Byron L Lam; Dean Eliott; Philip J Rosenfeld; Ninel Z Gregori; Jean-Pierre Hubschman; Janet L Davis; Gad Heilwell; Marc Spirn; Joseph Maguire; Roger Gay; Jane Bateman; Rosaleen M Ostrick; Debra Morris; Matthew Vincent; Eddy Anglade; Lucian V Del Priore; Robert Lanza
Journal:  Lancet       Date:  2014-10-15       Impact factor: 79.321

4.  Progression of Stargardt Disease as Determined by Fundus Autofluorescence in the Retrospective Progression of Stargardt Disease Study (ProgStar Report No. 9).

Authors:  Rupert W Strauss; Beatriz Muñoz; Alexander Ho; Anamika Jha; Michel Michaelides; Artur V Cideciyan; Isabelle Audo; David G Birch; Amir H Hariri; Muneeswar G Nittala; SriniVas Sadda; Sheila West; Hendrik P N Scholl
Journal:  JAMA Ophthalmol       Date:  2017-11-01       Impact factor: 7.389

5.  Stem Cell Ophthalmology Treatment Study (SCOTS): bone marrow derived stem cells in the treatment of Dominant Optic Atrophy.

Authors:  Jeffrey N Weiss; Steven Levy
Journal:  Stem Cell Investig       Date:  2019-12-05

6.  Clinical and molecular characteristics of childhood-onset Stargardt disease.

Authors:  Kaoru Fujinami; Jana Zernant; Ravinder K Chana; Genevieve A Wright; Kazushige Tsunoda; Yoko Ozawa; Kazuo Tsubota; Anthony G Robson; Graham E Holder; Rando Allikmets; Michel Michaelides; Anthony T Moore
Journal:  Ophthalmology       Date:  2014-10-12       Impact factor: 12.079

7.  Stem Cell Ophthalmology Treatment Study (SCOTS): bone marrow-derived stem cells in the treatment of Leber's hereditary optic neuropathy.

Authors:  Jeffrey N Weiss; Steven Levy; Susan C Benes
Journal:  Neural Regen Res       Date:  2016-10       Impact factor: 5.135

8.  Endogenous Mobilization of Bone-Marrow Cells Into the Murine Retina Induces Fusion-Mediated Reprogramming of Müller Glia Cells.

Authors:  Martina Pesaresi; Sergi A Bonilla-Pons; Giacoma Simonte; Daniela Sanges; Umberto Di Vicino; Maria Pia Cosma
Journal:  EBioMedicine       Date:  2018-02-28       Impact factor: 8.143

9.  Stem Cell Ophthalmology Treatment Study (SCOTS): Bone Marrow-Derived Stem Cells in the Treatment of Age-Related Macular Degeneration.

Authors:  Jeffrey N Weiss; Steven Levy
Journal:  Medicines (Basel)       Date:  2020-03-28
View more
  6 in total

Review 1.  Applying stem cell therapy in intractable diseases: a narrative review of decades of progress and challenges.

Authors:  Anna Pick Kiong Brianna; Ying Pei Ling
Journal:  Stem Cell Investig       Date:  2022-09-30

Review 2.  Current Status of Mesenchymal Stem/Stromal Cells for Treatment of Neurological Diseases.

Authors:  Milena B P Soares; Renata G J Gonçalves; Juliana F Vasques; Almir J da Silva-Junior; Fernanda Gubert; Girlaine Café Santos; Thaís Alves de Santana; Gabriela Louise Almeida Sampaio; Daniela Nascimento Silva; Massimo Dominici; Rosalia Mendez-Otero
Journal:  Front Mol Neurosci       Date:  2022-06-16       Impact factor: 6.261

Review 3.  Therapy Approaches for Stargardt Disease.

Authors:  Elena Piotter; Michelle E McClements; Robert E MacLaren
Journal:  Biomolecules       Date:  2021-08-09

Review 4.  Modulation of Mesenchymal Stem Cells for Enhanced Therapeutic Utility in Ischemic Vascular Diseases.

Authors:  Sally L Elshaer; Salma H Bahram; Pranav Rajashekar; Rajashekhar Gangaraju; Azza B El-Remessy
Journal:  Int J Mol Sci       Date:  2021-12-27       Impact factor: 5.923

Review 5.  Bone marrow-derived mononuclear stem cells in the treatment of retinal degenerations.

Authors:  Diego Garcia-Ayuso; Johnny Di Pierdomenico; David García-Bernal; Manuel Vidal-Sanz; María P Villegas-Pérez
Journal:  Neural Regen Res       Date:  2022-09       Impact factor: 5.135

Review 6.  New frontiers of retinal therapeutic intervention: a critical analysis of novel approaches.

Authors:  Onnisa Nanegrungsunk; Adrian Au; David Sarraf; Srinivas R Sadda
Journal:  Ann Med       Date:  2022-12       Impact factor: 5.348

  6 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.