Literature DB >> 33508569

"FLAMES: A novel burning entity in MOG IgG associated disease".

Kshiteeja Jain1, Ajith Cherian2, Divya K P3, Rajalakshmi P4, Bejoy Thomas5, Nandana J6.   

Abstract

FLAMES is a new clinico-radiological sub entity of myelin oligodendrocyte glycoprotein (MOG) antibody associated disease (MOGAD). FLAMES is characterized by fluid attenuated inversion recovery (FLAIR) imaging showing hyperintense cortical lesions, in MOG associated Encephalitis with Seizures. MOGAD usually presents with optic neuritis, myelitis or acute disseminated encephalomyelitis and such rare focal cortical encephalitis like presentation can be mistaken as due to viral aetiology. FLAMES can present with unilateral or bilateral cortical encephalitis and we report a case where magnetic resonance angiography, susceptibility weighted imaging and perfusion studies were done and the utility of these additional imaging markers in diagnosing FLAMES is discussed.
Copyright © 2021. Published by Elsevier B.V.

Entities:  

Keywords:  ASL hyperperfusion; FUEL,demyelination; MRI FLAIR; focal encephalitis; myelin oligodendrocyte

Year:  2021        PMID: 33508569     DOI: 10.1016/j.msard.2021.102759

Source DB:  PubMed          Journal:  Mult Scler Relat Disord        ISSN: 2211-0348            Impact factor:   4.339


  4 in total

1.  Rare autoimmune encephalitis presenting as fluid-attenuated inversion recovery-hyperintense lesions in anti-Myelin oligodendrocyte glycoprotein-associated encephalitis and seizures accompanied with anti-IgLON5 antibody.

Authors:  Wanyao Li; Wei Du; Yuhan Jiang; Yangyingqiu Liu; Na Liu; Yanwei Miao; Zhe Wang; Ying Wang
Journal:  Quant Imaging Med Surg       Date:  2022-07

Review 2.  Myelin Oligodendrocyte Glycoprotein-Associated Disorders.

Authors:  Erin Longbrake
Journal:  Continuum (Minneap Minn)       Date:  2022-08-01

3.  A case of unilateral recurrent cerebral cortical encephalitis with anti-myelin oligodendrocyte glycoprotein antibodies.

Authors:  Liying Guo; Ho Jun Yun; Xiaomu Tan; Xiaokun Geng; Yuchuan Ding
Journal:  Brain Circ       Date:  2022-06-30

4.  Myelin Oligodendrocyte Glycoprotein Antibody Associated Cerebral Cortical Encephalitis: Case Reports and Review of Literature.

Authors:  Hang Shu; Manqiu Ding; Pei Shang; Jia Song; Yue Lang; Li Cui
Journal:  Front Hum Neurosci       Date:  2022-01-03       Impact factor: 3.169

  4 in total

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