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Literature DB >> 33456165

Bowel perforation from malignant atrophic papulosis treated with eculizumab.

Ajithraj Sathiyaraj¹, Priyanga Jayakumar², Matthew R McGlennon¹, John F Eckford³, Sandy Itwaru Anne^3,4.

Abstract

We present the case of a 57-year-old man with known cutaneous manifestations of malignant atrophic papulosis, also known as Köhlmeier-Degos disease, who developed an almost-fatal small bowel perforation following a parathyroidectomy. He required two surgical interventions during his initial hospitalization and was started on eculizumab. Despite these therapies, the patient developed recurrent bowel perforations and ultimately died.

Entities: Chemical Disease Species

Keywords: Bowel perforation; Degos disease; eculizumab; malignant atrophic papulosis

Year: 2020 PMID： 33456165 PMCID： PMC7785204 DOI： 10.1080/08998280.2020.1809942

Source DB: PubMed Journal: Proc (Bayl Univ Med Cent) ISSN： 0899-8280

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References

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Bowel perforation from malignant atrophic papulosis treated with eculizumab.

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