Literature DB >> 33436030

Stakeholder perspectives on clinical research related to therapies for rare diseases: therapeutic misconception and the value of research.

Kylie Tingley1, Doug Coyle2, Ian D Graham2,3, Pranesh Chakraborty4,5,6, Kumanan Wilson2,3,7,8, Beth K Potter2.   

Abstract

BACKGROUND: For many rare diseases, few treatments are supported by strong evidence. Patients, family members, health care providers, and policy-makers thus have to consider whether to accept, recommend, or fund treatments with uncertain clinical effectiveness. They must also consider whether and how to contribute to clinical research that may involve receiving or providing the therapy being evaluated.
OBJECTIVE: To understand why and how patients and families with rare metabolic diseases, specialist metabolic physicians, and health policy advisors choose whether to participate in studies and how they use and value research.
METHODS: We conducted separate focus group interviews with each stakeholder group (three groups in total); two groups were conducted by telephone and the third was held in-person. Participants were recruited using purposive sampling. We analyzed each interview transcript sequentially using a qualitative description approach to inductively identify key themes. Several strategies to ensure credibility and trustworthiness were used including debriefing sessions after each focus group and having multiple team members review transcripts.
RESULTS: Four patients/caregivers, six physicians, and three policy advisors participated. Our findings did not support conventional perspectives that therapeutic misconception (gaining access to treatment) is the main motivating factor for patients/caregivers to participate in clinical research. Rather, patients'/caregivers' expressed reasons for participating in research included advancing science for the next generation and having an opportunity to share their experiences. Patients/caregivers and physicians described the difficulties in weighing risks versus benefits of accepting treatments not well-supported by evidence. Physicians also reported feeling conflicted in their dual role as patient advisor/advocate and evaluator of the evidence. Policy advisors were primarily focused on critically appraising the evidence to make recommendations for the health system.
CONCLUSIONS: Stakeholders differ in their perspectives on rare disease research but share concerns about the risks versus benefits of therapies when making individual- and population-level decisions.

Entities:  

Keywords:  Evidence-based medicine; Qualitative research; Rare diseases; Research participation; Therapeutic misconception

Mesh:

Year:  2021        PMID: 33436030      PMCID: PMC7805116          DOI: 10.1186/s13023-020-01624-0

Source DB:  PubMed          Journal:  Orphanet J Rare Dis        ISSN: 1750-1172            Impact factor:   4.123


  37 in total

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Review 2.  A framework for applying unfamiliar trial designs in studies of rare diseases.

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3.  Practical aspects of recruitment and retention in clinical trials of rare genetic diseases: the phenylketonuria (PKU) experience.

Authors:  Stephanie J DeWard; Ashley Wilson; Heather Bausell; Ashley S Volz; Kimberly Mooney
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4.  Standards for reporting qualitative research: a synthesis of recommendations.

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5.  Epidemiology of mucopolysaccharidoses.

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Journal:  Mol Genet Metab       Date:  2017-05-26       Impact factor: 4.797

Review 6.  Ethical issues of clinical trials in paediatric oncology from 2003 to 2013: a systematic review.

Authors:  Jean-Claude K Dupont; Kathy Pritchard-Jones; François Doz
Journal:  Lancet Oncol       Date:  2016-04-27       Impact factor: 41.316

Review 7.  Statistical challenges in the evaluation of treatments for small patient populations.

Authors:  Edward L Korn; Lisa M McShane; Boris Freidlin
Journal:  Sci Transl Med       Date:  2013-03-27       Impact factor: 17.956

8.  Advancing Telephone Focus Groups Method Through the Use of Webinar: Methodological Reflections on Evaluating Ontario, Canada's Healthy Babies Healthy Children Program.

Authors:  Eunice Chong; Adrienne Alayli-Goebbels; Lori Webel-Edgar; Sarah Muir; Heather Manson
Journal:  Glob Qual Nurs Res       Date:  2015-10-05

Review 9.  Using a meta-narrative literature review and focus groups with key stakeholders to identify perceived challenges and solutions for generating robust evidence on the effectiveness of treatments for rare diseases.

Authors:  Kylie Tingley; Doug Coyle; Ian D Graham; Lindsey Sikora; Pranesh Chakraborty; Kumanan Wilson; John J Mitchell; Sylvia Stockler-Ipsiroglu; Beth K Potter
Journal:  Orphanet J Rare Dis       Date:  2018-06-28       Impact factor: 4.123

10.  Clinical trials and medical care: defining the therapeutic misconception.

Authors:  Gail E Henderson; Larry R Churchill; Arlene M Davis; Michele M Easter; Christine Grady; Steven Joffe; Nancy Kass; Nancy M P King; Charles W Lidz; Franklin G Miller; Daniel K Nelson; Jeffrey Peppercorn; Barbra Bluestone Rothschild; Pamela Sankar; Benjamin S Wilfond; Catherine R Zimmer
Journal:  PLoS Med       Date:  2007-11-27       Impact factor: 11.069

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Review 2.  Ethical Issues in Care and Treatment of Neuronal Ceroid Lipofuscinoses (NCL)-A Personal View.

Authors:  Alfried Kohlschütter
Journal:  Front Neurol       Date:  2021-06-25       Impact factor: 4.003

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