| Literature DB >> 33273414 |
Alexander B Mohseny1, Dirk-Jan A Eikema2, Benedicte Neven3, Nicolaus Kröger4, Peter J Shaw5, Ghandi Damaj6, Jean-Hugues Dalle7, Paul V Bosman2, Fanny Delehaye8, Arjan C Lankester1, Frans J Smiers1, Regis Peffault de Latour9.
Abstract
Hepatitis-associated aplastic anemia (HAAA) has been reported in 23% to 33% of patients who received orthotopic liver transplantation (LT) for acute liver disease of unknown origin (nonviral hepatitis). In this situation, hematopoietic stem cell transplantation (HSCT) might be a curative option. Here the authors report on 6 patients who received HSCT after LT for nonviral HAAA hepatitis. The outcomes were interpreted in the context of recently reported immune suppressive therapy (IST) outcomes in 8 patients with HAAA and to HSCT outcomes in patients with HAAA who recovered from hepatitis without undergoing LT. All patients transplanted by using HLA-identical sibling donors (3 of 6) were alive and had normal liver function and hematopoiesis without graft versus host disease. Both patients receiving bone marrow from a matched unrelated donor (MUD) experienced extensive graft versus host disease that was fatal for one patient. Thereby, the authors conclude that HSCT can be considered as a first-choice treatment for this category of patients when HLA-identical donors are available. When no HLA-identical donor is available, IST should be applied as HSCT with other donor sources might be reserved for IST nonresponders or poor responders.Entities:
Mesh:
Year: 2021 PMID: 33273414 DOI: 10.1097/MPH.0000000000001991
Source DB: PubMed Journal: J Pediatr Hematol Oncol ISSN: 1077-4114 Impact factor: 1.289