Literature DB >> 33179224

[Prenatal diagnosis and genetic analysis of 17 fetuses with skeletal dysplasia].

Jianyang Lu1, Lei Huai, Caijuan Lu, Yafeng Wu, Huiqing Zhu, Xin Zhan, Hongbo Zhai.   

Abstract

OBJECTIVE: To explore strategies of prenatal genetic testing for fetuses featuring abnormal skeletal development.
METHODS: Clinical data of 17 fetuses with skeletal dysplasia was collected. The results of genetic testing and outcome of pregnancy were analyzed.
RESULTS: For 12 fetuses, the femur-to-foot length ratio was less than 0.9. Thirteen fetuses had a positive finding by genetic testing. One fetus was diagnosed with chromosomal aneuploidy, three were diagnosed with microdeletion/microduplications, and nine were diagnosed with hereditary bone diseases due to pathological variants of FGFR3, COL1A2, GPX4 or ALPL genes.
CONCLUSION: For fetuses with skeletal dysplasia characterized by short femur, in addition to chromosomal karyotyping and microarray analysis, sequencing of FGFR3 and other bone disease-related genes can improve the diagnostic rate.

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Year:  2020        PMID: 33179224     DOI: 10.3760/cma.j.cn511374-20191216-00639

Source DB:  PubMed          Journal:  Zhonghua Yi Xue Yi Chuan Xue Za Zhi        ISSN: 1003-9406


  1 in total

1.  Six ALPL gene variants in five children with hypophosphatasia.

Authors:  Na Su; Min Zhu; Xinran Cheng; Ke Xu; Roland Kocijan; Huijiao Zhang
Journal:  Ann Transl Med       Date:  2021-05
  1 in total

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