Literature DB >> 3316277

Cystic fibrosis.

M J Welsh1, R B Fick.   

Abstract

Entities:  

Mesh：

Year:  1987        PMID： 3316277      PMCID： PMC442419          DOI： 10.1172/JCI113237

Source DB:  PubMed          Journal:  J Clin Invest        ISSN： 0021-9738            Impact factor:   14.808


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  31 in total

1.  Demonstration of serum protein differences in cystic fibrosis by isoelectric focusing in thin-layer polyacrylamide gels.

Authors:  G B Wilson; T L Jahn; J R Fonseca
Journal:  Clin Chim Acta       Date:  1973-11-23       Impact factor: 3.786

Review 2.  Electrolyte transport by airway epithelia.

Authors:  M J Welsh
Journal:  Physiol Rev       Date:  1987-10       Impact factor: 37.312

3.  Improved patch-clamp techniques for high-resolution current recording from cells and cell-free membrane patches.

Authors:  O P Hamill; A Marty; E Neher; B Sakmann; F J Sigworth
Journal:  Pflugers Arch       Date:  1981-08       Impact factor: 3.657

4.  Relative ion permeability of normal and cystic fibrosis nasal epithelium.

Authors:  M Knowles; J Gatzy; R Boucher
Journal:  J Clin Invest       Date:  1983-05       Impact factor: 14.808

5.  Chloride impermeability in cystic fibrosis.

Authors:  P M Quinton
Journal:  Nature       Date:  1983-02-03       Impact factor: 49.962

6.  Higher bioelectric potentials due to decreased chloride absorption in the sweat glands of patients with cystic fibrosis.

Authors:  P M Quinton; J Bijman
Journal:  N Engl J Med       Date:  1983-05-19       Impact factor: 91.245

7.  The carbohydrate content of IgG from patients with cystic fibrosis.

Authors:  R Margolies; T F Boat
Journal:  Pediatr Res       Date:  1983-12       Impact factor: 3.756

8.  Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis.

Authors:  M Knowles; J Gatzy; R Boucher
Journal:  N Engl J Med       Date:  1981-12-17       Impact factor: 91.245

9.  Abnormal ion permeation through cystic fibrosis respiratory epithelium.

Authors:  M R Knowles; M J Stutts; A Spock; N Fischer; J T Gatzy; R C Boucher
Journal:  Science       Date:  1983-09-09       Impact factor: 47.728

10.  Fibroblasts from patients with I-cell disease and pseudo-Hurler polydystrophy are deficient in uridine 5'-diphosphate-N-acetylglucosamine: glycoprotein N-acetylglucosaminylphosphotransferase activity.

Authors:  M L Reitman; A Varki; S Kornfeld
Journal:  J Clin Invest       Date:  1981-05       Impact factor: 14.808
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  23 in total

1.  Quantitative analysis of inflammatory cells infiltrating the cystic fibrosis airway mucosa.

Authors:  C Hubeau; M Lorenzato; J P Couetil; D Hubert; D Dusser; E Puchelle; D Gaillard
Journal:  Clin Exp Immunol       Date:  2001-04       Impact factor: 4.330

2.  Dual modulation of chloride conductance by nucleotides in pancreatic and parotid zymogen granules.

Authors:  F Thévenod; K W Gasser; U Hopfer
Journal:  Biochem J       Date:  1990-11-15       Impact factor: 3.857

3.  Failure of cholinergic stimulation to induce a secretory response from the rectal mucosa in cystic fibrosis.

Authors:  J Hardcastle; P T Hardcastle; C J Taylor; J Goldhill
Journal:  Gut       Date:  1991-09       Impact factor: 23.059

4.  Enhanced intestinal glucose and alanine transport in cystic fibrosis.

Authors:  P Baxter; J Goldhill; J Hardcastle; P T Hardcastle; C J Taylor
Journal:  Gut       Date:  1990-07       Impact factor: 23.059

5.  Modulation of endocytic trafficking and apical stability of CFTR in primary human airway epithelial cultures.

Authors:  Deborah M Cholon; Wanda K O'Neal; Scott H Randell; John R Riordan; Martina Gentzsch
Journal:  Am J Physiol Lung Cell Mol Physiol       Date:  2009-12-11       Impact factor: 5.464

6.  Novel genetic determinants of low-level aminoglycoside resistance in Pseudomonas aeruginosa.

Authors:  Kristen N Schurek; Alexandra K Marr; Patrick K Taylor; Irith Wiegand; Lucie Semenec; Bhavjinder K Khaira; Robert E W Hancock
Journal:  Antimicrob Agents Chemother       Date:  2008-09-29       Impact factor: 5.191

7.  Diversity of airway epithelial cell targets for in vivo recombinant adenovirus-mediated gene transfer.

Authors:  A Mastrangeli; C Danel; M A Rosenfeld; L Stratford-Perricaudet; M Perricaudet; A Pavirani; J P Lecocq; R G Crystal
Journal:  J Clin Invest       Date:  1993-01       Impact factor: 14.808

8.  cAMP-dependent protein kinase inhibits the chloride conductance in apical membrane vesicles of human placenta.

Authors:  P Placchi; R Lombardo; A Tamanini; P Brusa; G Berton; G Cabrini
Journal:  J Membr Biol       Date:  1991-01       Impact factor: 1.843

9.  Cystic fibrosis-related diabetes: from CFTR dysfunction to oxidative stress.

Authors:  Thierry Ntimbane; Blandine Comte; Geneviève Mailhot; Yves Berthiaume; Vincent Poitout; Marc Prentki; Rémi Rabasa-Lhoret; Emile Levy
Journal:  Clin Biochem Rev       Date:  2009-11

10.  Extensive posttranscriptional deletion of the coding sequences for part of nucleotide-binding fold 1 in respiratory epithelial mRNA transcripts of the cystic fibrosis transmembrane conductance regulator gene is not associated with the clinical manifestations of cystic fibrosis.

Authors:  C S Chu; B C Trapnell; S M Curristin; G R Cutting; R G Crystal
Journal:  J Clin Invest       Date:  1992-09       Impact factor: 14.808
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