| Literature DB >> 33156480 |
Hemanta Kumar Nayak1, Sunil J Bhat1, Manas Kumar Panigrahi1, Imran Chouhan1, Chandan Kumar1, Subash Chandra Samal2.
Abstract
IgG4-related disease (IgG4 RD) is a multisystem disorder characterized by tumefactive (mass forming) lesions, storiform fibrosis, and IgG4-positive plasma cell infiltration. IgG4 sclerosing cholangitis (IgG4 SC) is the biliary manifestation of IgG4 RD, often in association with autoimmune pancreatitis (AIP). Here, we report two patients with IgG4-related cholangitis mimicking primary sclerosing cholangitis.Entities:
Keywords: Autoimmune pancreatitis; Cholestatic jaundice; IgG4 sclerosing cholangitis; Primary sclerosing cholangitis
Year: 2020 PMID: 33156480 DOI: 10.1007/s12664-020-01102-2
Source DB: PubMed Journal: Indian J Gastroenterol ISSN: 0254-8860