Literature DB >> 32949124

RFC1 expansions can mimic hereditary sensory neuropathy with cough and Sjögren syndrome.

Kishore R Kumar1,2,3,4, Andrea Cortese5,6, Susan E Tomlinson3,7, Stephanie Efthymiou5, Melina Ellis8, Danqing Zhu1, Marion Stoll1, Natalia Dominik5, Stephen Tisch7,9, Michel Tchan3,10, Kathy H C Wu9,11,12, Sophie Devery11, Penelope J Spring2, Simon Hawke3,13,14, Phillip Cremer3,15, Karl Ng3,15, Mary M Reilly5, Garth A Nicholson1,2,3,8, Henry Houlden5, Marina Kennerson1,3,8.   

Abstract

Entities:  

Year:  2020        PMID: 32949124      PMCID: PMC7586083          DOI: 10.1093/brain/awaa244

Source DB:  PubMed          Journal:  Brain        ISSN: 0006-8950            Impact factor:   13.501


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  7 in total

Review 1.  Proposed diagnostic criteria for cerebellar ataxia with neuropathy and vestibular areflexia syndrome (CANVAS).

Authors:  David J Szmulewicz; Leslie Roberts; Catriona A McLean; Hamish G MacDougall; G Michael Halmagyi; Elsdon Storey
Journal:  Neurol Clin Pract       Date:  2016-02

2.  Autosomal dominant hereditary sensory neuropathy with chronic cough and gastro-oesophageal reflux: clinical features in two families linked to chromosome 3p22-p24.

Authors:  Penelope J Spring; Cindy Kok; Garth A Nicholson; Alvin J Ing; Judith M Spies; Mark L Bassett; John Cameron; Paul Kerlin; Simon Bowler; Roger Tuck; John D Pollard
Journal:  Brain       Date:  2005-12       Impact factor: 13.501

3.  A locus for hereditary sensory neuropathy with cough and gastroesophageal reflux on chromosome 3p22-p24.

Authors:  C Kok; M L Kennerson; P J Spring; A J Ing; J D Pollard; G A Nicholson
Journal:  Am J Hum Genet       Date:  2003-07-17       Impact factor: 11.025

4.  Biallelic expansion of an intronic repeat in RFC1 is a common cause of late-onset ataxia.

Authors:  Roisin Sullivan; Jana Vandrovcova; Mary M Reilly; Andrea Cortese; Roberto Simone; Huma Tariq; Wai Yan Yau; Jack Humphrey; Zane Jaunmuktane; Prasanth Sivakumar; James Polke; Muhammad Ilyas; Eloise Tribollet; Pedro J Tomaselli; Grazia Devigili; Ilaria Callegari; Maurizio Versino; Vincenzo Salpietro; Stephanie Efthymiou; Diego Kaski; Nick W Wood; Nadja S Andrade; Elena Buglo; Adriana Rebelo; Alexander M Rossor; Adolfo Bronstein; Pietro Fratta; Wilson J Marques; Stephan Züchner; Henry Houlden
Journal:  Nat Genet       Date:  2019-03-29       Impact factor: 38.330

5.  Bioinformatics-Based Identification of Expanded Repeats: A Non-reference Intronic Pentamer Expansion in RFC1 Causes CANVAS.

Authors:  Haloom Rafehi; David J Szmulewicz; Mark F Bennett; Nara L M Sobreira; Kate Pope; Katherine R Smith; Greta Gillies; Peter Diakumis; Egor Dolzhenko; Michael A Eberle; María García Barcina; David P Breen; Andrew M Chancellor; Phillip D Cremer; Martin B Delatycki; Brent L Fogel; Anna Hackett; G Michael Halmagyi; Solange Kapetanovic; Anthony Lang; Stuart Mossman; Weiyi Mu; Peter Patrikios; Susan L Perlman; Ian Rosemergy; Elsdon Storey; Shaun R D Watson; Michael A Wilson; David S Zee; David Valle; David J Amor; Melanie Bahlo; Paul J Lockhart
Journal:  Am J Hum Genet       Date:  2019-06-20       Impact factor: 11.025

6.  Investigation of the RFC1 Repeat Expansion in a Canadian and a Brazilian Ataxia Cohort: Identification of Novel Conformations.

Authors:  Fulya Akçimen; Jay P Ross; Cynthia V Bourassa; Calwing Liao; Daniel Rochefort; Maria Thereza Drumond Gama; Marie-Josée Dicaire; Orlando G Barsottini; Bernard Brais; José Luiz Pedroso; Patrick A Dion; Guy A Rouleau
Journal:  Front Genet       Date:  2019-11-22       Impact factor: 4.599

7.  Cerebellar ataxia, neuropathy, vestibular areflexia syndrome due to RFC1 repeat expansion.

Authors:  Andrea Cortese; Stefano Tozza; Wai Yan Yau; Salvatore Rossi; Sarah J Beecroft; Zane Jaunmuktane; Zoe Dyer; Gianina Ravenscroft; Phillipa J Lamont; Stuart Mossman; Andrew Chancellor; Thierry Maisonobe; Yann Pereon; Cecile Cauquil; Silvia Colnaghi; Giulia Mallucci; Riccardo Curro; Pedro J Tomaselli; Gilbert Thomas-Black; Roisin Sullivan; Stephanie Efthymiou; Alexander M Rossor; Matilde Laurá; Menelaos Pipis; Alejandro Horga; James Polke; Diego Kaski; Rita Horvath; Patrick F Chinnery; Wilson Marques; Cristina Tassorelli; Grazia Devigili; Lea Leonardis; Nick W Wood; Adolfo Bronstein; Paola Giunti; Stephan Züchner; Tanya Stojkovic; Nigel Laing; Richard H Roxburgh; Henry Houlden; Mary M Reilly
Journal:  Brain       Date:  2020-02-01       Impact factor: 15.255

  7 in total
  7 in total

Review 1.  Genetic pain loss disorders.

Authors:  Annette Lischka; Petra Lassuthova; Arman Çakar; Christopher J Record; Jonas Van Lent; Jonathan Baets; Maike F Dohrn; Jan Senderek; Angelika Lampert; David L Bennett; John N Wood; Vincent Timmerman; Thorsten Hornemann; Michaela Auer-Grumbach; Yesim Parman; Christian A Hübner; Miriam Elbracht; Katja Eggermann; C Geoffrey Woods; James J Cox; Mary M Reilly; Ingo Kurth
Journal:  Nat Rev Dis Primers       Date:  2022-06-16       Impact factor: 65.038

Review 2.  Cough hypersensitivity and chronic cough.

Authors:  Kian Fan Chung; Lorcan McGarvey; Woo-Jung Song; Anne B Chang; Kefang Lai; Brendan J Canning; Surinder S Birring; Jaclyn A Smith; Stuart B Mazzone
Journal:  Nat Rev Dis Primers       Date:  2022-06-30       Impact factor: 65.038

Review 3.  An update on the neurological short tandem repeat expansion disorders and the emergence of long-read sequencing diagnostics.

Authors:  Sanjog R Chintalaphani; Sandy S Pineda; Ira W Deveson; Kishore R Kumar
Journal:  Acta Neuropathol Commun       Date:  2021-05-25       Impact factor: 7.801

Review 4.  Recessive cerebellar and afferent ataxias - clinical challenges and future directions.

Authors:  Marie Beaudin; Mario Manto; Jeremy D Schmahmann; Massimo Pandolfo; Nicolas Dupre
Journal:  Nat Rev Neurol       Date:  2022-03-24       Impact factor: 42.937

5.  Comprehensive genetic diagnosis of tandem repeat expansion disorders with programmable targeted nanopore sequencing.

Authors:  Igor Stevanovski; Sanjog R Chintalaphani; Hasindu Gamaarachchi; James M Ferguson; Sandy S Pineda; Carolin K Scriba; Michel Tchan; Victor Fung; Karl Ng; Andrea Cortese; Henry Houlden; Carol Dobson-Stone; Lauren Fitzpatrick; Glenda Halliday; Gianina Ravenscroft; Mark R Davis; Nigel G Laing; Avi Fellner; Marina Kennerson; Kishore R Kumar; Ira W Deveson
Journal:  Sci Adv       Date:  2022-03-04       Impact factor: 14.136

6.  RFC1-Related Disease: Molecular and Clinical Insights.

Authors:  Kayli Davies; David J Szmulewicz; Louise A Corben; Martin Delatycki; Paul J Lockhart
Journal:  Neurol Genet       Date:  2022-08-29

7.  Multi-type RFC1 repeat expansions as the most common cause of hereditary sensory and autonomic neuropathy.

Authors:  Jun-Hui Yuan; Yujiro Higuchi; Masahiro Ando; Eiji Matsuura; Akihiro Hashiguchi; Akiko Yoshimura; Tomonori Nakamura; Yusuke Sakiyama; Jun Mitsui; Hiroyuki Ishiura; Shoji Tsuji; Hiroshi Takashima
Journal:  Front Neurol       Date:  2022-08-17       Impact factor: 4.086

  7 in total

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