Literature DB >> 32613855

Krebs von den Lungen-6 as a biomarker for disease severity assessment in interstitial lung disease: a comprehensive review.

Miriana d'Alessandro1, Laura Bergantini1, Paolo Cameli1, Lucia Vietri1, Nicola Lanzarone1, Valerio Alonzi1, Maria Pieroni1, Rosa M Refini1, Piersante Sestini1, Francesco Bonella2, Elena Bargagli1.   

Abstract

Aim: Interstitial lung diseases (ILD) are a group of lung disorders characterized by interstitial lung thickening. Krebs von den Lungen-6 (KL-6) is a molecule that is predominantly expressed by damaged alveolar type II cells and it has been proposed as a potential biomarker of different ILD. Materials & methods: A growing literature about KL-6 has been reviewed and selected to evaluate its role in the clinical management of ILD to predict disease diagnosis, activity, prognosis and treatment response.
Results: KL-6 concentrations have been evaluated in fibrotic and granulomatous lung diseases and it was demonstrated to be a biomarker of disease severity useful for clinical follow-up of ILD patients. KL-6 levels differentiated between fibrotic ILD, such as idiopathic pulmonary fibrosis and chronic hypersensitivity pneumonitis, and nonfibrotic lung disorders, including sarcoidosis and pulmonary alveolar proteinosis.
Conclusion: KL-6 is predictive biomarker useful in the clinical management of ILD patients, in particular in patients with severe fibrotic lung disorders.

Entities:  

Keywords:  KL-6; hypersensitivity pneumonitis; idiopathic pulmonary fibrosis; interstitial lung diseases; pulmonary fibrosis associated with connective vascular diseases; sarcoidosis

Year:  2020        PMID: 32613855     DOI: 10.2217/bmm-2019-0545

Source DB:  PubMed          Journal:  Biomark Med        ISSN: 1752-0363            Impact factor:   2.851


  13 in total

1.  The Role of Serum Galectin-3 Levels in Patients with Sarcoidosis.

Authors:  Kaan Kara; Seda Tural Onur; Sinem Nedime Sokucu; Ozlem Kahya; Cengiz Ozdemir; Evin Ademoglu
Journal:  Med Princ Pract       Date:  2021-12-16       Impact factor: 1.927

2.  Extracellular Vesicle Surface Signatures in IPF Patients: A Multiplex Bead-Based Flow Cytometry Approach.

Authors:  Miriana d'Alessandro; Piera Soccio; Laura Bergantini; Paolo Cameli; Giulia Scioscia; Maria Pia Foschino Barbaro; Donato Lacedonia; Elena Bargagli
Journal:  Cells       Date:  2021-04-28       Impact factor: 6.600

3.  Serum Concentrations of KL-6 in Patients with IPF and Lung Cancer and Serial Measurements of KL-6 in IPF Patients Treated with Antifibrotic Therapy.

Authors:  Miriana d'Alessandro; Laura Bergantini; Paolo Cameli; Maria Pieroni; Rosa Metella Refini; Piersante Sestini; Elena Bargagli
Journal:  Cancers (Basel)       Date:  2021-02-09       Impact factor: 6.639

4.  Prognostic roles of KL-6 in disease severity and lung injury in COVID-19 patients: A longitudinal retrospective analysis.

Authors:  Kai Deng; Qinghong Fan; Yanhong Yang; Xizi Deng; Ruiying He; Yizhou Tan; Yun Lan; Xilong Deng; Yuejun Pan; Yaping Wang; Yujuan Guan; Huiyuan Liu; Fengjuan Chen; Xiaoneng Mo; Xinghua Tan; Chun Luo; Xueliang Wen; Ying Liu; Jinxin Liu; Lieguang Zhang; Xiaoping Tang; Fengyu Hu; Feng Li
Journal:  J Med Virol       Date:  2021-01-22       Impact factor: 2.327

5.  Baseline plasma KL-6 level predicts adverse outcomes in patients with idiopathic pulmonary fibrosis receiving nintedanib: a retrospective real-world cohort study.

Authors:  Tang-Hsiu Huang; Chin-Wei Kuo; Chian-Wei Chen; Yau-Lin Tseng; Chao-Liang Wu; Sheng-Hsiang Lin
Journal:  BMC Pulm Med       Date:  2021-05-15       Impact factor: 3.317

6.  Krebs von den Lungen-6 as Disease Severity Marker for COVID-19 Patients: Analytical Verification and Quality Assessment of the Tosoh AIA-360 Compared to Lumipulse G600II.

Authors:  Miriana d'Alessandro; Laura Bergantini; Dalila Cavallaro; Sara Gangi; Paolo Cameli; Edoardo Conticini; Bruno Frediani; Francesco Dotta; Elena Bargagli
Journal:  Int J Environ Res Public Health       Date:  2022-02-15       Impact factor: 3.390

Review 7.  Neutrophil Extracellular Traps in ANCA-Associated Vasculitis and Interstitial Lung Disease: A Scoping Review.

Authors:  Miriana d'Alessandro; Edoardo Conticini; Laura Bergantini; Paolo Cameli; Luca Cantarini; Bruno Frediani; Elena Bargagli
Journal:  Life (Basel)       Date:  2022-02-20

8.  Utility of serological biomarker' panels for diagnostic accuracy of interstitial lung diseases.

Authors:  Laura Bergantini; Miriana d'Alessandro; Lucia Vietri; Giuseppe Domenico Rana; Paolo Cameli; Silvia Acerra; Piersante Sestini; Elena Bargagli
Journal:  Immunol Res       Date:  2020-10-22       Impact factor: 2.829

9.  Clinical phenotyping in sarcoidosis management.

Authors:  Giuseppe Domenico Rana; Miriana d'Alessandro; Luigi Rizzi; Laura Bergantini; Paolo Cameli; Alfredo Vozza; Piersante Sestini; Patrizia Suppressa; Elena Bargagli
Journal:  Sarcoidosis Vasc Diffuse Lung Dis       Date:  2021-06-28       Impact factor: 0.670

10.  Peripheral biomarkers' panel for severe COVID-19 patients.

Authors:  Miriana d'Alessandro; Laura Bergantini; Paolo Cameli; Giuseppe Curatola; Lorenzo Remediani; Piersante Sestini; Elena Bargagli
Journal:  J Med Virol       Date:  2020-10-10       Impact factor: 20.693

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