Literature DB >> 32574866

A case of surgically resected cardiac rhabdomyoma with progressive left ventricular outflow tract obstruction.

Fazarina Mohammed1, Geok Chin Tan2, Kan N Hor3, Michael Arnold4, Yin Ping Wong5.   

Abstract

Cardiac rhabdomyoma is the most prevalent cardiac tumors in the pediatric population, in close association with tuberous sclerosis complex. It is usually detected antenatally or postnatally by echocardiography. Clinical presentations depend greatly on the size and position of the tumor mass. Interestingly, rhabdomyoma has a propensity to regress spontaneously and is not usually operated upon, unless the patient becomes hemodynamically compromised. Herein, we report an unusual case of surgically treated cardiac rhabdomyoma in a baby boy presented at birth with a progressive enlarging intraventricular mass, complicated with left ventricular outflow tract obstruction 7 weeks later. Histopathological examination of the intracardiac mass revealed sheets of tumor cells with spider-like morphology (known as "spider cells"), confirmed the diagnosis of rhabdomyoma. Close disease monitoring of patient's hemodynamic status in a newly diagnosed cardiac rhabdomyoma is inevitable as the tumor, although rare, may progress.
Copyright © 2020 Elsevier Inc. All rights reserved.

Entities:  

Keywords:  Cardiac tumor; Left ventricular outflow tract obstruction; Pediatric; Rhabdomyoma

Year:  2020        PMID: 32574866     DOI: 10.1016/j.carpath.2020.107226

Source DB:  PubMed          Journal:  Cardiovasc Pathol        ISSN: 1054-8807            Impact factor:   2.185


  1 in total

1.  Case report: multi-modality imaging of a right ventricular fibroma in a teenager.

Authors:  Yuexia Liu; Jiayao Shi; Huan Cen; Pengtao Sun
Journal:  Eur Heart J Case Rep       Date:  2022-06-29
  1 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.