| Literature DB >> 32574866 |
Fazarina Mohammed1, Geok Chin Tan2, Kan N Hor3, Michael Arnold4, Yin Ping Wong5.
Abstract
Cardiac rhabdomyoma is the most prevalent cardiac tumors in the pediatric population, in close association with tuberous sclerosis complex. It is usually detected antenatally or postnatally by echocardiography. Clinical presentations depend greatly on the size and position of the tumor mass. Interestingly, rhabdomyoma has a propensity to regress spontaneously and is not usually operated upon, unless the patient becomes hemodynamically compromised. Herein, we report an unusual case of surgically treated cardiac rhabdomyoma in a baby boy presented at birth with a progressive enlarging intraventricular mass, complicated with left ventricular outflow tract obstruction 7 weeks later. Histopathological examination of the intracardiac mass revealed sheets of tumor cells with spider-like morphology (known as "spider cells"), confirmed the diagnosis of rhabdomyoma. Close disease monitoring of patient's hemodynamic status in a newly diagnosed cardiac rhabdomyoma is inevitable as the tumor, although rare, may progress.Entities:
Keywords: Cardiac tumor; Left ventricular outflow tract obstruction; Pediatric; Rhabdomyoma
Year: 2020 PMID: 32574866 DOI: 10.1016/j.carpath.2020.107226
Source DB: PubMed Journal: Cardiovasc Pathol ISSN: 1054-8807 Impact factor: 2.185