Literature DB >> 32535587

Sleep-Disordered Breathing in Children with Prader-Willi Syndrome in Relation to Growth Hormone Therapy Onset.

Maja Zimmermann1, Constanze Laemmer2, Joachim Woelfle3, Rolf Fimmers4, Bettina Gohlke5.   

Abstract

OBJECTIVE: The aim of this study was to consider sleep apnea in Prader-Willi syndrome (PWS) children depending on age at growth hormone (GH) therapy onset. STUDY
DESIGN: We analyzed longitudinally cardiorespiratory polygraphy of 62 PWS children (aged 0-2.5 years at baseline). Twenty-one children (Group A) started GH-therapy during and 41 children (Group B) after their first year of life. Data were acquired before, at 3 and 6 months, then 1.2, 2.2, and 3.2 years after GH onset. Outcomes were determined with the obstructive apnea hypopnea index (OAHI), central apnea index (CAI), oxygen desaturation index (ODI), and by measuring obstructive sleep apnea (OSA) and peripheral blood oxygen saturation (SpO2).
RESULTS: We observed no significant differences in OAHI, CAI, ODI, and SpO2 depending on treatment onset. At baseline, 5/21 patients (23.8%) in Group A versus 15/41 patients (36.6%) in Group B showed pathological sleep apnea (OAHI ≥1.5). Pathological OSA increased significantly in Group A during the first 3 months of therapy but dropped below baseline after 1 year in both groups. ODI changed during GH therapy in both groups (from 4.0 to 2.6 in Group A, and 3.6 to 1.6 in Group B; baseline to 3.2 years; p < 0.05).
CONCLUSIONS: OSA in PWS children appears to develop independently of treatment onset. Treatment may therefore safely be initiated early but should be accompanied by regular sleep analysis.
© 2020 S. Karger AG, Basel.

Entities:  

Keywords:  Growth hormone therapy; Insulin-like growth factor-I; Obstructive sleep apnea; Prader-Willi syndrome

Mesh:

Substances:

Year:  2020        PMID: 32535587     DOI: 10.1159/000506943

Source DB:  PubMed          Journal:  Horm Res Paediatr        ISSN: 1663-2818            Impact factor:   2.852


  2 in total

Review 1.  Diagnosis and management of sleep disorders in Prader-Willi syndrome.

Authors:  Jessica Duis; Lara C Pullen; Maria Picone; Norman Friedman; Stephen Hawkins; Elise Sannar; Anna C Pfalzer; Althea Robinson Shelton; Deepan Singh; Phyllis C Zee; Daniel G Glaze; Amee Revana
Journal:  J Clin Sleep Med       Date:  2022-06-01       Impact factor: 4.324

2.  Sleep Challenges in Children with Prader-Willi Syndrome: A Patient and Family Handout.

Authors:  David G Ingram; Jill M Arganbright; Kelsee L Halpin; Caroline Okorie
Journal:  ATS Sch       Date:  2021-12-17
  2 in total

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