Literature DB >> 32497379

The World Federation of Hemophilia Annual Global Survey 1999-2018.

Jeffrey S Stonebraker1, Paula H B Bolton-Maggs2, Mark Brooker3, Bruce Evatt4, Alfonso Iorio5,6, Michael Makris7, Brian O'Mahony8,9, Mark W Skinner5,10, Donna Coffin11, Glenn F Pierce11, Ellia Tootoonchian11.   

Abstract

INTRODUCTION: The World Federation of Hemophilia (WFH) strives to achieve care for all patients with inherited bleeding disorders through research, advocacy, capacity building and education. The WFH developed and implemented the Annual Global Survey (AGS), through which comprehensive demographic and treatment data on bleeding disorders are collected each year from its constituent non-governmental national organizations. AIM: To describe the development, methodology and achievements of the WFH AGS over the past 20 years.
METHODS: The AGS is a yearly cross-sectional survey. Data are collected using a standardized form (available online and on paper), quality checked and reviewed, and published in English, French and Spanish. Over time, the AGS has been modified in response to changes in treatment landscape or emerging new issues.
RESULTS: Over the past 20 years, the AGS has reported an increase in the number of countries participating in the survey, a tripling in the number of people identified with rare bleeding disorders and an increase in the amount of factor used to treat people with haemophilia. Yet, a large treatment inequity gap still exists across the globe. In response to this gap, the WFH has analysed the AGS reports which has stimulated further development in quality of care indicators, estimates of the global prevalence of haemophilia, patient-level data collection efforts like the World Bleeding Disorders Registry and the Gene Therapy Registry.
CONCLUSION: The AGS has provided evidence to support research, programme planning and development activities of the WFH.
© 2020 John Wiley & Sons Ltd.

Entities:  

Keywords:  annual global survey; bleeding disorder; haemophilia; von Willebrand disease

Mesh:

Substances:

Year:  2020        PMID: 32497379     DOI: 10.1111/hae.14012

Source DB:  PubMed          Journal:  Haemophilia        ISSN: 1351-8216            Impact factor:   4.287


  9 in total

1.  Inhibitor; An Uncommon But Vexing Challenge In North Indian Patients With Hemophilia A.

Authors:  Debadrita Ray; Narender Kumar; Chander Hans; Anita Kler; Richa Jain; Deepak Bansal; Amita Trehan; Arihant Jain; Pankaj Malhotra; Jasmina Ahluwalia
Journal:  Indian J Hematol Blood Transfus       Date:  2022-05-06       Impact factor: 0.915

2.  [Consensus of Chinese expert on the diagnosis and treatment of rare bleeding disorders (version 2021)].

Authors: 
Journal:  Zhonghua Xue Ye Xue Za Zhi       Date:  2021-02-14

3.  Risk Factors for Amputation in the Surgical Treatment of Hemophilic Osteoarthropathy: A 20-Year Single-Center Report.

Authors:  Yiming Xu; Bin Feng; Wei Zhu; Yingjie Wang; Xisheng Weng
Journal:  Pain Res Manag       Date:  2022-03-28       Impact factor: 3.037

4.  The experiences of people with haemophilia and their families of gene therapy in a clinical trial setting: regaining control, the Exigency study.

Authors:  Simon Fletcher; Kathryn Jenner; Luke Pembroke; Michael Holland; Kate Khair
Journal:  Orphanet J Rare Dis       Date:  2022-04-04       Impact factor: 4.123

Review 5.  The Impact of Recombinant Versus Plasma-Derived Factor VIII Concentrates on Inhibitor Development in Previously Untreated Patients With Hemophilia A: A 2021 Update of a Systematic Review and Meta-Analysis.

Authors:  Kelvin Kohar; Stephanie A Prayogo; Lowilius Wiyono
Journal:  Cureus       Date:  2022-06-16

6.  Gene therapy - are we ready now?

Authors:  Radoslaw Kaczmarek
Journal:  Haemophilia       Date:  2022-05       Impact factor: 4.263

7.  Content analysis of identity challenges in patients with haemophilia: A qualitative study.

Authors:  Roya Dolatkhah; Reza Shabanloei; Hossein Ebrahimi; Mostafa Ghasempour
Journal:  Nurs Open       Date:  2021-01-06

8.  Real-World Rates of Bleeding, Factor VIII Use, and Quality of Life in Individuals with Severe Haemophilia A Receiving Prophylaxis in a Prospective, Noninterventional Study.

Authors:  Gili Kenet; Yeu-Chin Chen; Gillian Lowe; Charles Percy; Huyen Tran; Annette von Drygalski; Marc Trossaërt; Mark Reding; Johannes Oldenburg; Maria Eva Mingot-Castellano; Young-Shil Park; Flora Peyvandi; Margareth C Ozelo; Johnny Mahlangu; Jennifer Quinn; Mei Huang; Divya B Reddy; Benjamin Kim
Journal:  J Clin Med       Date:  2021-12-18       Impact factor: 4.241

9.  Haemophilia in France: Modelisation of the Clinical Pathway for Patients.

Authors:  Karen Beny; Benjamin du Sartz de Vigneulles; Florence Carrouel; Denis Bourgeois; Valérie Gay; Claude Negrier; Claude Dussart
Journal:  Int J Environ Res Public Health       Date:  2022-01-06       Impact factor: 3.390

  9 in total

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