Literature DB >> 32479166

Long-Term Rituximab Use to Maintain Remission of Antineutrophil Cytoplasmic Antibody-Associated Vasculitis: A Randomized Trial.

Pierre Charles1, Élodie Perrodeau2, Maxime Samson3, Bernard Bonnotte3, Antoine Néel4, Christian Agard5, Antoine Huart6, Alexandre Karras7, François Lifermann8, Pascal Godmer9, Pascal Cohen10, Catherine Hanrotel-Saliou11, Nicolas Martin-Silva12, Grégory Pugnet6, François Maurier13, Jean Sibilia14, Pierre-Louis Carron15, Pierre Gobert16, Nadine Meaux-Ruault17, Thomas Le Gallou18, Stéphane Vinzio19, Jean-François Viallard20, Eric Hachulla21, Christine Vinter10, Xavier Puéchal10, Benjamin Terrier10, Philippe Ravaud2, Luc Mouthon10, Loïc Guillevin10.   

Abstract

BACKGROUND: Biannual rituximab infusions over 18 months effectively maintain remission after a "standard" remission induction regimen for patients with antineutrophil cytoplasmic antibody-associated vasculitis (AAV).
OBJECTIVE: To evaluate the efficacy of prolonged rituximab therapy in preventing AAV relapses in patients with granulomatosis with polyangiitis (GPA) or microscopic polyangiitis (MPA) who have achieved complete remission after completing an 18-month maintenance regimen.
DESIGN: Randomized controlled trial. (ClinicalTrials.gov: NCT02433522).
SETTING: 39 clinical centers in France. PATIENTS: 68 patients with GPA and 29 with MPA who achieved complete remission after the first phase of maintenance therapy. INTERVENTION: Rituximab or placebo infusion every 6 months for 18 months (4 infusions). MEASUREMENTS: The primary end point was relapse-free survival at month 28. Relapse was defined as new or reappearing symptoms or worsening disease, with a Birmingham Vasculitis Activity Score greater than 0.
RESULTS: From March 2015 to April 2016, 97 patients (mean age, 63.9 years; 35% women) were randomly assigned, 50 to the rituximab and 47 to the placebo group. Relapse-free survival estimates at month 28 were 96% (95% CI, 91% to 100%) and 74% (CI, 63% to 88%) in the rituximab and placebo groups, respectively, an absolute difference of 22% (CI, 9% to 36%) with a hazard ratio of 7.5 (CI, 1.67 to 33.7) (P = 0.008). Major relapse-free survival estimates at month 28 were 100% (CI, 93% to 100%) versus 87% (CI, 78% to 97%) (P = 0.009), respectively. At least 1 serious adverse event developed in 12 patients (24%) in the rituximab group (with 9 infectious serious adverse events occurring among 6 patients [12%]) versus 14 patients (30%) in the placebo group (with 6 infectious serious adverse events developing among 4 patients [9%]). No deaths occurred in either group. LIMITATION: Potential selection bias based on previous rituximab response and tolerance.
CONCLUSION: Extended therapy with biannual rituximab infusions over 18 months was associated with a lower incidence of AAV relapse compared with standard maintenance therapy. PRIMARY FUNDING SOURCE: French Ministry of Health and Hoffmann-La Roche.

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Year:  2020        PMID: 32479166     DOI: 10.7326/M19-3827

Source DB:  PubMed          Journal:  Ann Intern Med        ISSN: 0003-4819            Impact factor:   25.391


  25 in total

Review 1.  French recommendations for the management of systemic necrotizing vasculitides (polyarteritis nodosa and ANCA-associated vasculitides).

Authors:  Benjamin Terrier; Raphaël Darbon; Cécile-Audrey Durel; Eric Hachulla; Alexandre Karras; Hélène Maillard; Thomas Papo; Xavier Puechal; Grégory Pugnet; Thomas Quemeneur; Maxime Samson; Camille Taille; Loïc Guillevin
Journal:  Orphanet J Rare Dis       Date:  2020-12-29       Impact factor: 4.123

Review 2.  Novel Therapies for ANCA-associated Vasculitis.

Authors:  Sara Monti; Fabio Brandolino; Alessandra Milanesi; Blerina Xoxi; Paolo Delvino; Carlomaurizio Montecucco
Journal:  Curr Rheumatol Rep       Date:  2021-04-28       Impact factor: 4.592

Review 3.  [Biologics for connective tissue diseases and vasculitides].

Authors:  Bernhard Hellmich; Joerg C Henes
Journal:  Internist (Berl)       Date:  2022-01-14       Impact factor: 0.743

4.  What Is the Best Maintenance Therapy for ANCA Vasculitis?

Authors:  Katti Woerner; Patrick H Nachman
Journal:  Clin J Am Soc Nephrol       Date:  2021-11-09       Impact factor: 8.237

5.  Disease Activity and Adverse Events in Patients with ANCA-Associated Vasculitides Undergoing Long-Term Dialysis.

Authors:  Maëlis Kauffmann; Mickaël Bobot; Thomas Robert; Stéphane Burtey; Grégoire Couvrat-Desvergnes; Frédéric Lavainne; Xavier Puéchal; Benjamin Terrier; Thomas Quéméneur; Stanislas Faguer; Alexandre Karras; Philippe Brunet; Cécile Couchoud; Noémie Jourde-Chiche
Journal:  Clin J Am Soc Nephrol       Date:  2021-11       Impact factor: 8.237

6.  Rituximab in the Frail and Elderly with Severe ANCA-Associated GN.

Authors:  Silke R Brix; Vladimir Tesař
Journal:  Clin J Am Soc Nephrol       Date:  2022-08-02       Impact factor: 10.614

7.  The effect of achieving serological remission on subsequent risk of relapse, end-stage renal disease and mortality in ANCA-associated vasculitis: a target trial emulation study.

Authors:  Gregory McDermott; Xiaoqing Fu; Claire Cook; Catherine Ahola; Brett Doliner; Jennifer Hanberg; John H Stone; Hyon K Choi; Yuqing Zhang; Zachary S Wallace
Journal:  Ann Rheum Dis       Date:  2022-06-13       Impact factor: 27.973

8.  Evaluation of Rituximab for Induction and Maintenance Therapy in Patients 75 Years and Older With Antineutrophil Cytoplasmic Antibody-Associated Vasculitis.

Authors:  Sara Thietart; Alexandre Karras; Jean-François Augusto; Carole Philipponnet; Pierre-Louis Carron; Xavier Delbrel; Rafik Mesbah; Gilles Blaison; Pierre Duffau; Khalil El Karoui; Perrine Smets; Jonathan London; Luc Mouthon; Loïc Guillevin; Benjamin Terrier; Xavier Puéchal
Journal:  JAMA Netw Open       Date:  2022-07-01

9.  Serious infections in ANCA-associated vasculitides in the biologic era: real-life data from a multicenter cohort of 162 patients.

Authors:  Evangelia Argyriou; Noemin Kapsala; Konstantinos Thomas; Alexandros Panagiotopoulos; Aglaia Chalkia; Emilia Hadziyannis; Kyriaki Boki; Pelagia Katsimbri; Dimitrios T Boumpas; Panagiota Giannou; Dimitrios Petras; Dimitrios Vassilopoulos
Journal:  Arthritis Res Ther       Date:  2021-03-20       Impact factor: 5.156

Review 10.  Treatment Updates in Antineutrophil Cytoplasmic Autoantibodies (ANCA) Vasculitis.

Authors:  Koyal Jain; Pankaj Jawa; Vimal K Derebail; Ronald J Falk
Journal:  Kidney360       Date:  2021-04-29
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