Literature DB >> 32474284

NMOSD or GFAP astrocytopathy? A case report.

Yue Zhang1, Abhijeet Kumar Bhekharee2, Xiang Zhang3.   

Abstract

We describe a 43-year-old female whose manifestations fulfilled the diagnostic criteria of aquaporin-4 IgG negative neuromyelitis optica spectrum disorders (NMOSD). High titer of glial fibrillary acidic protein (GFAP) antibody was detected in cerebrospinal fluid. In this case, some symptoms pertained to NMOSD and some to GFAP antibody-related disorders. The patient had a good response to corticosteroids.
Copyright © 2020 Elsevier B.V. All rights reserved.

Entities:  

Keywords:  Aquaporin-4 IgG negative neuromyelitis optica spectrum disorders; Glial fibrillary acidic protein antibody

Mesh:

Substances:

Year:  2020        PMID: 32474284     DOI: 10.1016/j.msard.2020.102202

Source DB:  PubMed          Journal:  Mult Scler Relat Disord        ISSN: 2211-0348            Impact factor:   4.339


  2 in total

Review 1.  Area Postrema Syndrome in Autoimmune Glial Fibrillary Acidic Protein Astrocytopathy: A Case Series and Literature Review.

Authors:  Bo Deng; Jingguo Wang; Hai Yu; Lei Jin; Yue Qiu; Xiaoni Liu; Pengyu Wang; Xiang Zhang; Xiangjun Chen
Journal:  Neurol Neuroimmunol Neuroinflamm       Date:  2022-09-26

2.  Autoimmune glial fibrillary acidic protein astrocytopathy in children: a retrospective study.

Authors:  Xiamei Zhuang; Ke Jin; Xiaoming Li; Junwei Li
Journal:  Eur J Med Res       Date:  2022-01-22       Impact factor: 2.175

  2 in total

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