Literature DB >> 3221243

Microangiopathy with encephalopathy, hearing loss and retinal arteriolar occlusions: two new cases.

H Heiskala1, H Somer, J Kovanen, E Poutiainen, H Karli, M Haltia.   

Abstract

Two young women developed encephalopathy, hearing loss and retinal arteriolar occlusions. Their behaviour became immature and cognitive functions were severely impaired. One of the patients underwent brain biopsy, which showed several microinfarcts in both white and grey matter and microangiopathic changes, with thickened arteriolar segments staining intensely for laminin and fibronectin. These findings support the concept of a new type of microangiopathy involving the brain, inner ear and retina.

Entities:  

Mesh：

Year:  1988        PMID： 3221243     DOI： 10.1016/0022-510x(88)90102-5

Source DB:  PubMed          Journal:  J Neurol Sci        ISSN： 0022-510X            Impact factor:   3.181


  9 in total

1.  Encephalopathy, hearing loss and retinal occlusions (Susac's syndrome): a new case.

Authors:  M Maddestra; S Sabatini; A Paci
Journal:  Ital J Neurol Sci       Date:  1998-08

Review 2.  [Susac syndrome: an interdisciplinary challenge].

Authors:  J Dörr; S Jarius; B Wildemann; E B Ringelstein; W Schwindt; M Deppe; K P Wandinger; J Promesberger; F Paul; I Kleffner
Journal:  Nervenarzt       Date:  2011-10       Impact factor: 1.214

Review 3.  Characteristics of Susac syndrome: a review of all reported cases.

Authors:  Jan Dörr; Sarah Krautwald; Brigitte Wildemann; Sven Jarius; Marius Ringelstein; Thomas Duning; Orhan Aktas; Erich Bernd Ringelstein; Friedemann Paul; Ilka Kleffner
Journal:  Nat Rev Neurol       Date:  2013-04-30       Impact factor: 42.937

4.  Encephalopathy, deafness and blindness in young women: a distinct retinocochleocerebral arteriolopathy?

Authors:  J Bogousslavsky; J M Gaio; L R Caplan; F Regli; M Hommel; T R Hedges; M Ferrazzini; P Pollak
Journal:  J Neurol Neurosurg Psychiatry       Date:  1989-01       Impact factor: 10.154

5.  Encephalopathy, visual disturbance and hearing loss-recognizing the symptoms of Susac syndrome.

Authors:  Jan Dörr; Helena Radbruch; Markus Bock; Jens Wuerfel; Anne Brüggemann; Klaus P Wandinger; Daniel Zeise; Caspar F Pfueller; Frauke Zipp; Friedemann Paul
Journal:  Nat Rev Neurol       Date:  2009-12       Impact factor: 42.937

6.  Evolution of lesions in Susac syndrome at serial MR imaging with diffusion-weighted imaging and apparent diffusion coefficient values.

Authors:  Matthew L White; Yan Zhang; Wendy R K Smoker
Journal:  AJNR Am J Neuroradiol       Date:  2004-05       Impact factor: 3.825

7.  Treatment of Susac's Syndrome.

Authors:  Robert M Rennebohm; Robert A Egan; John O Susac
Journal:  Curr Treat Options Neurol       Date:  2008-01       Impact factor: 3.598

8.  A fatal case of Susac syndrome: The importance of ophthalmic examination in confirming the diagnosis.

Authors:  Ryan A Shields; Robert A Kleinman; Stephen J Smith; Steven R Sanislo; Quan Dong Nguyen
Journal:  Am J Ophthalmol Case Rep       Date:  2018-07-24

9.  Aggressive immunosuppressive treatment of Susac's syndrome in an adolescent: using treatment of dermatomyositis as a model.

Authors:  Robert M Rennebohm; Martin Lubow; Jerome Rusin; Lisa Martin; Deborah M Grzybowski; John O Susac
Journal:  Pediatr Rheumatol Online J       Date:  2008-01-29       Impact factor: 3.054
  9 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.