Literature DB >> 32153686

Adult-onset Still's disease revealed by a complete atrioventricular block, totally regressive under corticosteroid therapy.

Pierre-Guillaume Piriou1, Julien Plessis1, Vincent Letocart1, Nicolas Piriou1, Vincent Probst1, Antoine Néel2.   

Abstract

We report the case of a 40-year-old veterinary surgeon who was admitted for spiking fevers, arthralgia, and a complete atrioventricular block. Tests revealed an inflammatory syndrome, hepatic cytolysis, neutrophilic leukocytosis, and increased troponin levels. Cardiac magnetic resonance imaging showed a small myocarditis but no tissue abnormality on the conduction pathways. In the absence of evidence-based infection and favorable evolution under broad spectrum antibiotherapy, an adult-onset Still's disease was suspected and corticosteroid therapy administered. Evolution was then impressively favorable, with a persistent sinus heart rhythm 3 days later. Learning objective: Febrile conductive disorders occurring during a systemic disorder with negative infection and auto-immunity work-up should lead to consider an adult-onset Still's disease, which can be treated and cured, especially with steroids. Moreover, fever, polyarthritis, neutrophilic leukocytosis, pericarditis, and myocarditis should lead to consideration of adult-onset Still's disease.
© 2019 Japanese College of Cardiology. Published by Elsevier Ltd. All rights reserved.

Entities:  

Keywords:  Adult-onset Still’s disease; Atrioventricular block; Myocarditis; Spiking fever; Steroid

Year:  2019        PMID: 32153686      PMCID: PMC7054654          DOI: 10.1016/j.jccase.2019.11.004

Source DB:  PubMed          Journal:  J Cardiol Cases        ISSN: 1878-5409


  5 in total

1.  Adult-onset Still's disease and myocarditis: successful treatment with intravenous immunoglobulin and maintenance of remission with etanercept.

Authors:  A Kuek; A Weerakoon; K Ahmed; A J K Ostör
Journal:  Rheumatology (Oxford)       Date:  2007-04-19       Impact factor: 7.580

2.  Complete atrioventricular block and aseptic meningitis in a patient with adult-onset Still's disease and concurrent hemophagocytic syndrome.

Authors:  Haruka Tsuchiya; Hirotaka Tsuno; Syunta Kaneko; Hiroyuki Yamashita; Yuko Takahashi; Toshikazu Kano; Akio Mimori
Journal:  Mod Rheumatol       Date:  2014-02-18       Impact factor: 3.023

3.  Fatal myocarditis in adult-onset Still disease with diffuse intravascular coagulation.

Authors:  Matteo Colina; Marcello Govoni; Francesco Trotta
Journal:  Rheumatol Int       Date:  2008-12-02       Impact factor: 2.631

Review 4.  Myocarditis in adult-onset still disease.

Authors:  Mathieu Gerfaud-Valentin; Pascal Sève; Jean Iwaz; Anne Gagnard; Christiane Broussolle; Isabelle Durieu; Jacques Ninet; Arnaud Hot
Journal:  Medicine (Baltimore)       Date:  2014-10       Impact factor: 1.889

5.  Diagnostic and management of life-threatening Adult-Onset Still Disease: a French nationwide multicenter study and systematic literature review.

Authors:  Antoine Néel; Anaïs Wahbi; Benoit Tessoulin; Julien Boileau; Dorothée Carpentier; Olivier Decaux; Laurence Fardet; Guillaume Geri; Pascal Godmer; Cécile Goujard; Hervé Maisonneuve; Arnaud Mari; Jacques Pouchot; Jean-Marc Ziza; Cédric Bretonnière; Mohamed Hamidou
Journal:  Crit Care       Date:  2018-04-11       Impact factor: 9.097

  5 in total
  1 in total

Review 1.  New insights on multigenic autoinflammatory diseases.

Authors:  Petros Efthimiou; Olga Petryna; Priscila Nakasato; Apostolos Kontzias
Journal:  Ther Adv Musculoskelet Dis       Date:  2022-09-03       Impact factor: 3.625

  1 in total

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