Literature DB >> 31811084

Monitoring Complement Activation: The New Conundrum in Thrombotic Microangiopathies.

Fadi Fakhouri1, Véronique Frémeaux-Bacchi2.   

Abstract

Entities:  

Keywords:  alternative complement pathway; atypical hemolytic uremic syndrome; complement; complement activation; eculizumab; hemolytic uremic syndrome; humanized monoclonal antibodies; nephrologists; risk factors; thrombotic microangiopathies; thrombotic microangiopathy

Year:  2019        PMID: 31811084      PMCID: PMC6895483          DOI: 10.2215/CJN.12111019

Source DB:  PubMed          Journal:  Clin J Am Soc Nephrol        ISSN: 1555-9041            Impact factor:   8.237


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  11 in total

1.  The genetics of the alternative pathway of complement in the pathogenesis of HELLP syndrome.

Authors:  Francesca Crovetto; Nicolò Borsa; Barbara Acaia; Carla Nishimura; Kathy Frees; Richard J H Smith; Flora Peyvandi; Roberta Palla; Massimo Cugno; Silvana Tedeschi; Pierangela Castorina; Edgardo Somigliana; Gianluigi Ardissino; Luigi Fedele
Journal:  J Matern Fetal Neonatal Med       Date:  2012-06-07

2.  Factor H, membrane cofactor protein, and factor I mutations in patients with hemolysis, elevated liver enzymes, and low platelet count syndrome.

Authors:  Fadi Fakhouri; Mathieu Jablonski; Jacques Lepercq; Jacques Blouin; Alexandra Benachi; Maryvonne Hourmant; Yves Pirson; Antoine Dürrbach; Jean-Pierre Grünfeld; Bertrand Knebelmann; Véronique Frémeaux-Bacchi
Journal:  Blood       Date:  2008-07-24       Impact factor: 22.113

3.  Soluble c5b-9 as a biomarker for complement activation in atypical hemolytic uremic syndrome.

Authors:  Fengxiao Bu; Nicole C Meyer; Yuzhou Zhang; Nicolo Ghiringhelli Borsa; Christie Thomas; Carla Nester; Richard J H Smith
Journal:  Am J Kidney Dis       Date:  2015-03-25       Impact factor: 8.860

4.  Atypical haemolytic uraemic syndrome and pregnancy: outcome with ongoing eculizumab.

Authors:  Aude Servais; Nadège Devillard; Véronique Frémeaux-Bacchi; Aurélie Hummel; Laurent Salomon; Cécile Contin-Bordes; Hélène Gomer; Christophe Legendre; Yahsou Delmas
Journal:  Nephrol Dial Transplant       Date:  2016-09-01       Impact factor: 5.992

5.  Complement Activation and Thrombotic Microangiopathies.

Authors:  Marta Palomo; Miquel Blasco; Patricia Molina; Miquel Lozano; Manuel Praga; Sergi Torramade-Moix; Julia Martinez-Sanchez; Joan Cid; Gines Escolar; Enric Carreras; Cristina Paules; Fatima Crispi; Luis F Quintana; Esteban Poch; Lida Rodas; Emma Goma; Johann Morelle; Mario Espinosa; Enrique Morales; Ana Avila; Virginia Cabello; Gema Ariceta; Sara Chocron; Joaquin Manrique; Xoana Barros; Nadia Martin; Ana Huerta; Gloria M Fraga-Rodriguez; Mercedes Cao; Marisa Martin; Ana Maria Romera; Francesc Moreso; Anna Manonelles; Eduard Gratacos; Arturo Pereira; Josep M Campistol; Maribel Diaz-Ricart
Journal:  Clin J Am Soc Nephrol       Date:  2019-11-06       Impact factor: 8.237

6.  Pathogenic Variants in Complement Genes and Risk of Atypical Hemolytic Uremic Syndrome Relapse after Eculizumab Discontinuation.

Authors:  Fadi Fakhouri; Marc Fila; François Provôt; Yahsou Delmas; Christelle Barbet; Valérie Châtelet; Cédric Rafat; Mathilde Cailliez; Julien Hogan; Aude Servais; Alexandre Karras; Raifah Makdassi; Feriell Louillet; Jean-Philippe Coindre; Eric Rondeau; Chantal Loirat; Véronique Frémeaux-Bacchi
Journal:  Clin J Am Soc Nephrol       Date:  2016-10-31       Impact factor: 8.237

Review 7.  Haemolytic uraemic syndrome.

Authors:  Fadi Fakhouri; Julien Zuber; Véronique Frémeaux-Bacchi; Chantal Loirat
Journal:  Lancet       Date:  2017-02-25       Impact factor: 79.321

8.  Modified Ham test for atypical hemolytic uremic syndrome.

Authors:  Eleni Gavriilaki; Xuan Yuan; Zhaohui Ye; Alexander J Ambinder; Satish P Shanbhag; Michael B Streiff; Thomas S Kickler; Alison R Moliterno; C John Sperati; Robert A Brodsky
Journal:  Blood       Date:  2015-04-10       Impact factor: 22.113

9.  Dynamics of complement activation in aHUS and how to monitor eculizumab therapy.

Authors:  Marina Noris; Miriam Galbusera; Sara Gastoldi; Paolo Macor; Federica Banterla; Elena Bresin; Claudio Tripodo; Serena Bettoni; Roberta Donadelli; Elisabetta Valoti; Francesco Tedesco; Alessandro Amore; Rosanna Coppo; Piero Ruggenenti; Eliana Gotti; Giuseppe Remuzzi
Journal:  Blood       Date:  2014-07-18       Impact factor: 22.113

10.  Mutations in complement regulatory proteins predispose to preeclampsia: a genetic analysis of the PROMISSE cohort.

Authors:  Jane E Salmon; Cara Heuser; Michael Triebwasser; M Kathryn Liszewski; David Kavanagh; Lubka Roumenina; D Ware Branch; Tim Goodship; Veronique Fremeaux-Bacchi; John P Atkinson
Journal:  PLoS Med       Date:  2011-03-22       Impact factor: 11.069

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