Literature DB >> 31594657

Assessment of liver phenotype in adults with severe alpha-1 antitrypsin deficiency (Pi*ZZ genotype).

Julia Kümpers1, Malin Fromme1, Carolin V Schneider1, Christian Trautwein1, Helmut Denk2, Karim Hamesch1, Pavel Strnad3.   

Abstract

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Year:  2019        PMID: 31594657     DOI: 10.1016/j.jhep.2019.08.011

Source DB:  PubMed          Journal:  J Hepatol        ISSN: 0168-8278            Impact factor:   25.083


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  5 in total

Review 1.  Non-Invasive Assessment and Management of Liver Involvement in Adults With Alpha-1 Antitrypsin Deficiency.

Authors:  Karim Hamesch; Pavel Strnad
Journal:  Chronic Obstr Pulm Dis       Date:  2020-07

2.  Non-invasive testing for liver pathology in alpha-1 antitrypsin deficiency.

Authors:  Syed Hamza Abbas; Elisha Pickett; David A Lomas; Douglas Thorburn; Bibek Gooptu; John R Hurst; Aileen Marshall
Journal:  BMJ Open Respir Res       Date:  2020-12

Review 3.  Obstacles to Early Diagnosis and Treatment of Alpha-1 Antitrypsin Deficiency: Current Perspectives.

Authors:  Mark Quinn; Paul Ellis; Anita Pye; Alice M Turner
Journal:  Ther Clin Risk Manag       Date:  2020-12-16       Impact factor: 2.423

Review 4.  Liver Fibrosis-From Mechanisms of Injury to Modulation of Disease.

Authors:  Christian Liedtke; Yulia A Nevzorova; Tom Luedde; Henning Zimmermann; Daniela Kroy; Pavel Strnad; Marie-Luise Berres; Jürgen Bernhagen; Frank Tacke; Jacob Nattermann; Ulrich Spengler; Tilman Sauerbruch; Alexander Wree; Zeinab Abdullah; René H Tolba; Jonel Trebicka; Twan Lammers; Christian Trautwein; Ralf Weiskirchen
Journal:  Front Med (Lausanne)       Date:  2022-01-11

5.  Mild Iron Overload as Seen in Individuals Homozygous for the Alpha-1 Antitrypsin Pi*Z Variant Does Not Promote Liver Fibrogenesis in HFE Knockout Mice.

Authors:  Nurdan Guldiken; Karim Hamesch; Shari Malan Schuller; Mahmoud Aly; Cecilia Lindhauer; Carolin V Schneider; Malin Fromme; Christian Trautwein; Pavel Strnad
Journal:  Cells       Date:  2019-11-09       Impact factor: 6.600

  5 in total

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