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Literature DB >> 3156059

Immunological alterations in a case of Papillon-Lefèvre syndrome with recurrent cutaneous infections.

G Borroni, A Pagani, A Carcaterra, R Pericoli, P Gabba, M Marconi.

Abstract

An immunological study was performed in a 16-year-old boy affected with Papillon-Lefèvre syndrome (PLS) and recurrent staphylococcal cutaneous infections. A defect of neutrophil intracellular killing of Staphylococcus aureus and a decreased lymphocyte proliferative response to phytohaemagglutinin were detected. The possible role of these alterations in promoting recurrent infections in PLS is discussed.

Entities: Disease Species

Mesh：

Year: 1985 PMID： 3156059 DOI： 10.1159/000249491

Source DB: PubMed Journal: Dermatologica ISSN： 0011-9075

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Cited

5 in total

1. Role of polymorphonuclear leukocyte-derived serine proteinases in defense against Actinobacillus actinomycetemcomitans.

Authors: Susanne F de Haar; Pieter S Hiemstra; Martijn T J M van Steenbergen; Vincent Everts; Wouter Beertsen
Journal: Infect Immun Date: 2006-09 Impact factor: 3.441

Immunological alterations in a case of Papillon-Lefèvre syndrome with recurrent cutaneous infections.

1. Role of polymorphonuclear leukocyte-derived serine proteinases in defense against Actinobacillus actinomycetemcomitans.

Review 2. Infections in patients with inherited defects in phagocytic function.

3. Identification of novel mutation in cathepsin C gene causing Papillon-Lefèvre Syndrome in Mexican patients.

4. Papillon-Lefevre syndrome: A case report of 2 affected siblings.

5. A novel mutation in the cathepsin C (CTSC) gene in Iranian family with Papillon-Lefevre syndrome.