Literature DB >> 31456526

Diagnostic Approach to the Patients with Suspected Primary Immunodeficiency.

Marzieh Tavakol1,2, Mahnaz Jamee3, Gholamreza Azizi1,4, Homa Sadri1,2, Yasser Bagheri5, Majid Zaki-Dizaji6, Fatemeh Sadat Mahdavi3, Farhad Jadidi-Niaragh7, Sanaz Tajfirooz8, Ali N Kamali9, Fatemeh Aghamahdi1,10, Shahab Noorian10, Habibeh Taghavi Kojidi10, Mehdi Mosavian1,11, Rahman Matani11, Elahe Dolatshahi12, Kumars Porrostami8, Nasrin Elahimehr8, Marzie Fatemi-Abhari8, Laleh Sharifi13, Reza Arjmand14, Sabahat Haghi15, Hamed Zainaldain4, Reza Yazdani4, Mohammadreza Shaghaghi16, Hassan Abolhassani17, Asghar Aghamohammadi4.   

Abstract

BACKGROUND AND
OBJECTIVE: Primary immunodeficiency diseases (PIDs) are a group of more than 350 disorders affecting distinct components of the innate and adaptive immune systems. In this review, the classic and advanced stepwise approach towards the diagnosis of PIDs are simplified and explained in detail.
RESULTS: Susceptibility to recurrent infections is the main hallmark of almost all PIDs. However, noninfectious complications attributable to immune dysregulation presenting with lymphoproliferative and/or autoimmune disorders are not uncommon. Moreover, PIDs could be associated with misleading presentations including allergic manifestations, enteropathies, and malignancies.
CONCLUSION: Timely diagnosis is the most essential element in improving outcome and reducing the morbidity and mortality in PIDs. This wouldn't be possible unless the physicians keep the diagnosis of PID in mind and be sufficiently aware of the approach to these patients. Copyright© Bentham Science Publishers; For any queries, please email at epub@benthamscience.net.

Entities:  

Keywords:  Primary immunodeficiency disorders; antibody deficiency; autoimmunity; combined immunodeficiency; enteropathy; infection.

Year:  2020        PMID： 31456526     DOI： 10.2174/1871530319666190828125316

Source DB:  PubMed          Journal:  Endocr Metab Immune Disord Drug Targets        ISSN： 1871-5303            Impact factor:   2.895


  4 in total

1.  Evaluation of the 10 Warning Signs in Primary and Secondary Immunodeficient Patients.

Authors:  Fadime Ceyda Eldeniz; Yahya Gul; Alaaddin Yorulmaz; Sukru Nail Guner; Sevgi Keles; Ismail Reisli
Journal:  Front Immunol       Date:  2022-05-13       Impact factor: 8.786

2.  COVID-19 Vaccination in Patients with Rheumatic Diseases Leads to a High Seroconversion Rate and Reduced Self-Imposed Isolation and Shielding Behavior.

Authors:  Christian Ammitzbøll; Marianne Kragh Thomsen; Jakob Bøgh Andersen; Lars Erik Bartels; Marie-Louise From Hermansen; Anders Dahl Johannsen; Clara Elbæk Mistegaard; Susan Mikkelsen; Signe Risbøl Vils; Christian Erikstrup; Ellen-Margrethe Hauge; Anne Troldborg
Journal:  Mod Rheumatol       Date:  2022-07-21       Impact factor: 2.862

3.  T-follicular helper cell expansion and chronic T-cell activation are characteristic immune anomalies in Evans syndrome.

Authors:  Deepak Kumar; Chengyu Prince; Carolyn M Bennett; Michael Briones; Laura Lucas; Athena Russell; Kiran Patel; Satheesh Chonat; Sara Graciaa; Holly Edington; Michael H White; Lisa Kobrynski; Manar Abdalgani; Suhag Parikh; Sharat Chandra; Jack Bleesing; Rebecca Marsh; Sunita Park; Edmund K Waller; Sampath Prahalad; Shanmuganathan Chandrakasan
Journal:  Blood       Date:  2022-01-20       Impact factor: 22.113

4.  Impaired Antibody Response to the BNT162b2 Messenger RNA Coronavirus Disease 2019 Vaccine in Patients With Systemic Lupus Erythematosus and Rheumatoid Arthritis.

Authors:  Christian Ammitzbøll; Lars Erik Bartels; Jakob Bøgh Andersen; Signe Risbøl Vils; Clara Elbaek Mistegård; Anders Dahl Johannsen; Marie-Louise From Hermansen; Marianne Kragh Thomsen; Christian Erikstrup; Ellen-Margrethe Hauge; Anne Troldborg
Journal:  ACR Open Rheumatol       Date:  2021-07-17
  4 in total

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