Literature DB >> 31392489

Cystic fibrosis transmembrane conductance regulator modulates enteric cholinergic activities and is abnormally expressed in the enteric ganglia of patients with slow transit constipation.

Ka Ming Yeh1, Olle Johansson2, Huy Le1, Karan Rao1, Irit Markus1, Dayashan Shevy Perera3, David Zachary Lubowski3, Denis Warwick King3, Li Zhang4, Hongzhuan Chen5, Lu Liu6.   

Abstract

BACKGROUND: Cystic fibrosis transmembrane conductance regulator (CFTR) was recently found in the enteric nervous system, where its role is unclear. We aimed to identify which enteric neuronal structures express CFTR, whether CFTR modulates enteric neurotransmission and if altered CFTR expression is associated with slow transit constipation (STC).
METHODS: Immunofluorescence double labeling was performed to localize CFTR with various neuronal and glial cell markers in the human colon. The immunoreactivity (IR) of CFTR and choline acetyltransferase (ChAT) on myenteric plexus of control and STC colon was quantitatively analyzed. In control colonic muscle strips, electrical field stimulation (EFS) evoked contractile responses and the release of acetylcholine (ACh) was measured in the presence of the CFTR channel inhibitor, CFTR(inh)-172.
RESULTS: CFTR-IR was densely localized to myenteric ganglia, where it was co-localized with neuronal markers HuC/D and β-tubulin, and glial marker S-100 but little with glial fibrillary acidic protein. Vesicular ACh transport was almost exclusively co-localized with CFTR, but neurons expressing nitric oxide synthase were CFTR negative. Significant reductions of CFTR-IR (P < 0.01) and ChAT-IR (P < 0.05) were observed on myenteric ganglia of STC compared to control. Pre-treatment of colonic muscle strips with CFTR(inh)-172 (10 µM) significantly inhibited EFS-evoked contractile responses (P < 0.01) and ACh release (P < 0.05).
CONCLUSIONS: Co-localization of CFTR-IR with cholinergic markers, inhibition of EFS-induced colonic muscle contractility and ACh release by CFTR(inh)-172 suggest that CFTR modulates enteric cholinergic neurotransmission. The downregulation of CFTR and ChAT in myenteric ganglia of STC correlated with the impaired contractile responses to EFS.

Entities:  

Keywords:  CFTR; Motility disorder; Slow transit constipation

Mesh:

Substances:

Year:  2019        PMID: 31392489     DOI: 10.1007/s00535-019-01610-9

Source DB:  PubMed          Journal:  J Gastroenterol        ISSN: 0944-1174            Impact factor:   7.527


  52 in total

1.  Ca2+ transients in myenteric glial cells during the colonic migrating motor complex in the isolated murine large intestine.

Authors:  Matthew J Broadhead; Peter O Bayguinov; Takanobu Okamoto; Dante J Heredia; Terence K Smith
Journal:  J Physiol       Date:  2011-11-07       Impact factor: 5.182

2.  Measurement of cystic fibrosis transmembrane conductance regulator activity using fluorescence spectrophotometry.

Authors:  Ángel G Valdivieso; María C Marín; Mariángeles Clauzure; Tomás A Santa-Coloma
Journal:  Anal Biochem       Date:  2011-07-30       Impact factor: 3.365

3.  Linaclotide-a novel secretagogue in the treatment of irritable bowel syndrome with constipation and chronic idiopathic constipation.

Authors:  Shivani Sharma; Tina Sharma; Richa Dhingra; Prince Tomar; Sukhminder Singh; Manav Malhotra; T R Bhardwaj
Journal:  Mini Rev Med Chem       Date:  2013-10       Impact factor: 3.862

4.  Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA.

Authors:  J R Riordan; J M Rommens; B Kerem; N Alon; R Rozmahel; Z Grzelczak; J Zielenski; S Lok; N Plavsic; J L Chou
Journal:  Science       Date:  1989-09-08       Impact factor: 47.728

5.  Altered eicosanoid metabolism in the cystic fibrosis mouse small intestine.

Authors:  Robert C De Lisle; Lauren Meldi; Maureen Flynn; Kyle Jansson
Journal:  J Pediatr Gastroenterol Nutr       Date:  2008-10       Impact factor: 2.839

6.  Amniotic fluid digestive enzyme analysis is useful for identifying CFTR gene mutations of unclear significance.

Authors:  Florine Oca; Sophie Dreux; Bénédicte Gérard; Brigitte Simon-Bouy; Alix de Becdelièvre; Claude Ferec; Emmanuelle Girodon; Françoise Muller
Journal:  Clin Chem       Date:  2009-10-15       Impact factor: 8.327

7.  Plasmodium falciparum-activated chloride channels are defective in erythrocytes from cystic fibrosis patients.

Authors:  Patrick Verloo; Clemens H M Kocken; Annemarie Van der Wel; Ben C Tilly; Boris M Hogema; Maarten Sinaasappel; Alan W Thomas; Hugo R De Jonge
Journal:  J Biol Chem       Date:  2003-12-16       Impact factor: 5.157

8.  Role of tyrosine phosphorylation in the muscarinic activation of the cystic fibrosis transmembrane conductance regulator (CFTR).

Authors:  Arnaud Billet; Yishan Luo; Haouaria Balghi; John W Hanrahan
Journal:  J Biol Chem       Date:  2013-06-11       Impact factor: 5.157

9.  Defective CFTR expression and function are detectable in blood monocytes: development of a new blood test for cystic fibrosis.

Authors:  Claudio Sorio; Mario Buffelli; Chiara Angiari; Michele Ettorre; Jan Johansson; Marzia Vezzalini; Laura Viviani; Mario Ricciardi; Genny Verzè; Baroukh Maurice Assael; Paola Melotti
Journal:  PLoS One       Date:  2011-07-21       Impact factor: 3.240

10.  CFTR activator increases intestinal fluid secretion and normalizes stool output in a mouse model of constipation.

Authors:  Onur Cil; Puay-Wah Phuan; Sujin Lee; Joseph Tan; Peter M Haggie; Marc H Levin; Liang Sun; Jay R Thiagarajah; Tonghui Ma; A S Verkman
Journal:  Cell Mol Gastroenterol Hepatol       Date:  2016-01-09
View more
  4 in total

Review 1.  Luminal Gastrointestinal Manifestations of Cystic Fibrosis.

Authors:  Samuel J Burton; Christine Hachem; James M Abraham
Journal:  Curr Gastroenterol Rep       Date:  2021-03-23

Review 2.  Intestinal Inflammation and Alterations in the Gut Microbiota in Cystic Fibrosis: A Review of the Current Evidence, Pathophysiology and Future Directions.

Authors:  Rachel Y Tam; Josie M van Dorst; Isabelle McKay; Michael Coffey; Chee Y Ooi
Journal:  J Clin Med       Date:  2022-01-27       Impact factor: 4.241

3.  Ji-Chuan decoction ameliorates slow transit constipation via regulation of intestinal glial cell apoptosis.

Authors:  Xiu-Min Wang; Li-Xia Lv; Yue-Si Qin; Yu-Zhu Zhang; Ni Yang; Shu Wu; Xiu-Wen Xia; Hong Yang; Hong Xu; Ying Liu; Wei-Jun Ding
Journal:  World J Gastroenterol       Date:  2022-09-14       Impact factor: 5.374

Review 4.  What Do We Know about the Microbiome in Cystic Fibrosis? Is There a Role for Probiotics and Prebiotics?

Authors:  Josie M van Dorst; Rachel Y Tam; Chee Y Ooi
Journal:  Nutrients       Date:  2022-01-22       Impact factor: 5.717

  4 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.