| Literature DB >> 31377012 |
Samuel Shribman1, Evan Reid2, Andrew H Crosby3, Henry Houlden4, Thomas T Warner5.
Abstract
Hereditary spastic paraplegia (HSP) describes a heterogeneous group of genetic neurodegenerative diseases characterised by progressive spasticity of the lower limbs. The pathogenic mechanism, associated clinical features, and imaging abnormalities vary substantially according to the affected gene and differentiating HSP from other genetic diseases associated with spasticity can be challenging. Next generation sequencing-based gene panels are now widely available but have limitations and a molecular diagnosis is not made in most suspected cases. Symptomatic management continues to evolve but with a greater understanding of the pathophysiological basis of individual HSP subtypes there are emerging opportunities to provide targeted molecular therapies and personalised medicine.Entities:
Mesh:
Year: 2019 PMID: 31377012 DOI: 10.1016/S1474-4422(19)30235-2
Source DB: PubMed Journal: Lancet Neurol ISSN: 1474-4422 Impact factor: 44.182