Literature DB >> 31348448

Acroangiodermatitis of Mali and Stewart-Bluefarb syndrome.

Emily P Chea1, Veronica L Rutt1, Joshua Levin1, Richard McClain1, Stephen M Purcell2.   

Abstract

Acroangiodermatitis (AAD), also known as pseudo-Kaposi sarcoma, is a rare benign vascular proliferation mainly of the extremities. It is characterized by violaceous patches or plaques resembling Kaposi sarcoma. The term pseudo-Kaposi sarcoma encompasses 2 variants of acroangiodermatitis: Mali type and Stewart-Bluefarb syndrome (SBS). Mali-type AAD is more common and is associated with chronic venous hypertension, while SBS is more rare and is associated with arteriovenous malformations and iatrogenic arteriovenous fistulae. We report 2 patients, representing each type of AAD.

Entities:  

Year:  2019        PMID: 31348448

Source DB:  PubMed          Journal:  Cutis        ISSN: 0011-4162


  1 in total

1.  Dusky erythematous plaques over the lower leg associated with bony deformity.

Authors:  T Dev; S Arava; N Bhari
Journal:  J Postgrad Med       Date:  2022 Jan-Mar       Impact factor: 1.476

  1 in total

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