Literature DB >> 31278024

Transient liver injury and severe neonatal cholestasis in infant with glucose-6-phosphate dehydrogenase deficiency due to a new mutation.

D Ben Fredj1, C Barro2, P Joly3, N Thomassin4, S Collardeau-Frachon5, D Plantaz6, D Adjaoud6.   

Abstract

We report the case of a neonate with a new, previously undescribed, glucose-6-phosphate dehydrogenase (G6PD) gene mutation, which was revealed by severe cholestasis, hyperbilirubinemia, and transient liver dysfunction. The severity of the clinical phenotype with ongoing chronic hemolytic anemia suggests that this mutation belongs to class 1 G6PD deficiency. The hemizygous mutation «c.675G>c; p.Trp225Cys» was detected by genomic sequencing. Since severe G6PD deficiency can be revealed by cholestasis, it is important to check G6PD enzyme activity when faced with a case of liver dysfunction in the neonatal period.
Copyright © 2019. Published by Elsevier Masson SAS.

Entities:  

Keywords:  Cholestasis; G6PD deficiency; Hemolysis; Hyperbilirubinemia; Liver insufficiency; New mutation

Mesh:

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Year:  2019        PMID: 31278024     DOI: 10.1016/j.arcped.2019.05.005

Source DB:  PubMed          Journal:  Arch Pediatr        ISSN: 0929-693X            Impact factor:   1.180


  1 in total

1.  Etiology of neonatal cholestasis after emerging molecular diagnostics.

Authors:  Huanhuan Wang; Lin Yang; Jin Wang
Journal:  Transl Pediatr       Date:  2022-03
  1 in total

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