Literature DB >> 31239560

The value of diagnostic testing for parents of children with rare genetic diseases.

Deborah A Marshall1, Karen V MacDonald2, Sebastian Heidenreich3,4, Taila Hartley5, Francois P Bernier6, Meredith K Gillespie5, Brenda McInnes6, A Micheil Innes6, Christine M Armour5, Kym M Boycott5.   

Abstract

PURPOSE: Exome sequencing (ES) can rapidly identify disease-causing variants responsible for rare, single-gene diseases, and potentially reduce the duration of the diagnostic odyssey. Our study examines how parents and families value ES.
METHODS: We developed a discrete choice experiment (DCE) survey that was administered to parents of children with rare diseases. The DCE included 14 choice tasks with 6 attributes and 3 alternatives. A valuation-space model was used to estimate willingness to pay, willingness to wait for test results, and minimum acceptable chance of a diagnosis for changes in each attribute.
RESULTS: There were n = 319 respondents of whom 89% reported their child had genetic testing, and 66% reported their child had a diagnosis. Twenty-six percent reported that their child had been offered ES. Parents were willing to pay CAD$6590 (US$4943), wait 5.2 years to obtain diagnostic test results, and accept a reduction of 3.1% in the chance of a diagnosis for ES compared with operative procedures.
CONCLUSION: Timely access to ES could reduce the diagnostic odyssey and associated costs. Before ES is incorporated routinely into care for patients with rare diseases in Canada and more broadly, there must be a clear understanding of its value to patients and families.

Entities:  

Keywords:  children; exome sequencing; genetic diseases; genetic testing; patient preferences

Mesh:

Year:  2019        PMID: 31239560     DOI: 10.1038/s41436-019-0583-1

Source DB:  PubMed          Journal:  Genet Med        ISSN: 1098-3600            Impact factor:   8.822


  12 in total

1.  Current Practices for Accounting for Preference Heterogeneity in Health-Related Discrete Choice Experiments: A Systematic Review.

Authors:  Suzana Karim; Benjamin M Craig; Caroline Vass; Catharina G M Groothuis-Oudshoorn
Journal:  Pharmacoeconomics       Date:  2022-08-12       Impact factor: 4.558

2.  A Systematic Review of Discrete Choice Experiments and Conjoint Analysis on Genetic Testing.

Authors:  Semra Ozdemir; Jia Jia Lee; Isha Chaudhry; Remee Rose Quintana Ocampo
Journal:  Patient       Date:  2021-06-04       Impact factor: 3.883

3.  Preferences and values for rapid genomic testing in critically ill infants and children: a discrete choice experiment.

Authors:  Ilias Goranitis; Stephanie Best; John Christodoulou; Tiffany Boughtwood; Zornitza Stark
Journal:  Eur J Hum Genet       Date:  2021-04-02       Impact factor: 4.246

4.  Genetic skin disorders: The value of a multidisciplinary clinic.

Authors:  James Clayton Parker; Sneha Rangu; Katheryn Lynn Grand; Elizabeth Joyce Bhoj; Leslie Castelo-Soccio; Sarah E Sheppard
Journal:  Am J Med Genet A       Date:  2021-01-27       Impact factor: 2.802

5.  Genome-Wide Sequencing for Unexplained Developmental Disabilities or Multiple Congenital Anomalies: A Health Technology Assessment.

Authors: 
Journal:  Ont Health Technol Assess Ser       Date:  2020-03-06

6.  Opportunities and pitfalls of social media research in rare genetic diseases: a systematic review.

Authors:  Emily G Miller; Amanda L Woodward; Grace Flinchum; Jennifer L Young; Holly K Tabor; Meghan C Halley
Journal:  Genet Med       Date:  2021-07-19       Impact factor: 8.864

Review 7.  The influence of social determinants of health on the genetic diagnostic odyssey: who remains undiagnosed, why, and to what effect?

Authors:  Yarden S Fraiman; Monica H Wojcik
Journal:  Pediatr Res       Date:  2020-09-15       Impact factor: 3.756

Review 8.  Genomic Health Literacy Interventions in Pediatrics: Scoping Review.

Authors:  Aarushi Gupta; Joseph A Cafazzo; Maarten J IJzerman; Joost F Swart; Sebastiaan Vastert; Nico M Wulffraat; Susanne Benseler; Deborah Marshall; Rae Yeung; Marinka Twilt
Journal:  J Med Internet Res       Date:  2021-12-24       Impact factor: 5.428

9.  Toward the diagnosis of rare childhood genetic diseases: what do parents value most?

Authors:  Samantha Pollard; Deirdre Weymann; Jessica Dunne; Fatemeh Mayanloo; John Buckell; James Buchanan; Sarah Wordsworth; Jan M Friedman; Sylvia Stockler-Ipsiroglu; Nick Dragojlovic; Alison M Elliott; Mark Harrison; Larry D Lynd; Dean A Regier
Journal:  Eur J Hum Genet       Date:  2021-04-26       Impact factor: 4.246

10.  Initial experience from a renal genetics clinic demonstrates a distinct role in patient management.

Authors:  Christie P Thomas; Margaret E Freese; Agnes Ounda; Jennifer G Jetton; Myrl Holida; Lama Noureddine; Richard J Smith
Journal:  Genet Med       Date:  2020-03-17       Impact factor: 8.822

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