Literature DB >> 3118237

Myelopathy due to diffuse thickening of the cervical dura mater in Maroteaux-Lamy syndrome: report of a case.

N Tamaki1, N Kojima, M Tanimoto, T Suyama, S Matsumoto.   

Abstract

A rare case of diffuse thickening of the cervical dura mater leading to cord compression in Maroteaux-Lamy syndrome (mucopolysaccharidosis VI) is reported. Spinal computed tomographic scans after intrathecal metrizamide injection and magnetic resonance images are shown. This condition presents as cervical myelopathy. Early decompression can be beneficial for patients with this infrequent metabolic disorder.

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Year:  1987        PMID： 3118237     DOI： 10.1227/00006123-198709000-00027

Source DB:  PubMed          Journal:  Neurosurgery        ISSN： 0148-396X            Impact factor:   4.654


  4 in total

1.  Anesthetic management of a child with Maroteau-Lamy syndrome.

Authors:  M Shiga; K Mikawa; N Maekawa; O Tanaka; R Goto; H Yaku; H Obara
Journal:  J Anesth       Date:  1992-07       Impact factor: 2.078

2.  Mucopolysaccharidosis: thickening of dura mater at the craniocervical junction and other CT/MRI findings.

Authors:  A Taccone; P Tortori Donati; A Marzoli; A Dell'Acqua; R Gatti; D Leone
Journal:  Pediatr Radiol       Date:  1993

3.  Craniocervical decompression in patients with mucopolysaccharidosis VI: development of a scoring system to determine indication and outcome of surgery.

Authors:  Christina Lampe; Christian Lampe; Manfred Schwarz; Wibke Müller-Forell; Paul Harmatz; Eugen Mengel
Journal:  J Inherit Metab Dis       Date:  2013-02-14       Impact factor: 4.982

Review 4.  Pathogenesis and treatment of spine disease in the mucopolysaccharidoses.

Authors:  Sun H Peck; Margret L Casal; Neil R Malhotra; Can Ficicioglu; Lachlan J Smith
Journal:  Mol Genet Metab       Date:  2016-06-04       Impact factor: 4.797
  4 in total

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