Literature DB >> 3107856

Immunological comparison of biotinidase in serum from normal and biotinidase-deficient individuals.

B Wolf, J B Miller, J Hymes, J Secor McVoy, Y Ishikawa, E Shapira.   

Abstract

An antiserum specific to enzymatically active human serum biotinidase was prepared. Using this antiserum, two immunologically cross-reacting protein fractions, only one of which corresponds to the active enzyme, were observed in sera from individuals with normal biotinidase activity. Neither of these protein fractions was detected in sera from 18 individuals with biotinidase deficiency from 15 families.

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Year:  1987        PMID： 3107856     DOI： 10.1016/0009-8981(87)90104-5

Source DB:  PubMed          Journal:  Clin Chim Acta        ISSN： 0009-8981            Impact factor:   3.786


  5 in total

1.  Comparison of patients with complete and partial biotinidase deficiency: biochemical studies.

Authors:  T M Suormala; E R Baumgartner; H Wick; S Scheibenreiter; S Schweitzer
Journal:  J Inherit Metab Dis       Date:  1990       Impact factor: 4.982

2.  Biochemical and immunological characterization of serum biotinidase in profound biotinidase deficiency.

Authors:  P S Hart; J Hymes; B Wolf
Journal:  Am J Hum Genet       Date:  1992-01       Impact factor: 11.025

3.  Prospective ascertainment of complete and partial serum biotinidase deficiency in the newborn.

Authors:  G Dunkel; C R Scriver; C L Clow; S Melançon; B Lemieux; A Grenier; C Laberge
Journal:  J Inherit Metab Dis       Date:  1989       Impact factor: 4.982

4.  Co-purification of human serum lipoamidase and biotinidase: evidence that the two enzyme activities are due to the same enzyme protein.

Authors:  L Nilsson; B Kågedal
Journal:  Biochem J       Date:  1993-04-15       Impact factor: 3.857

5.  Role of human serum biotinidase as biotin-binding protein.

Authors:  J Chauhan; K Dakshinamurti
Journal:  Biochem J       Date:  1988-11-15       Impact factor: 3.857
  5 in total

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