Literature DB >> 3106713

Normal dolichol concentration in urine sediments from four patients with neuronal ceroid lipofuscinosis (Batten's disease).

B C Paton, A Poulos.   

Abstract

The dolichol contents of urine sediments from a patient with infantile (Santavuori), a patient with late infantile (Jansky-Bielschowsky) and two patients with juvenile (Spielmeyer-Vogt) neuronal ceroid lipofuscinosis (Batten's disease) were not elevated when compared to those from healthy controls.

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Year:  1987        PMID： 3106713     DOI： 10.1007/bf01799485

Source DB:  PubMed          Journal:  J Inherit Metab Dis        ISSN： 0141-8955            Impact factor:   4.982


  11 in total

1.  A simple method for the isolation and purification of total lipides from animal tissues.

Authors:  J FOLCH; M LEES; G H SLOANE STANLEY
Journal:  J Biol Chem       Date:  1957-05       Impact factor: 5.157

2.  Elevated urinary dolichol levels in chronic alcoholics.

Authors:  R K Pullarkat; S Raguthu
Journal:  Alcohol Clin Exp Res       Date:  1985 Jan-Feb       Impact factor: 3.455

3.  Dolichol metabolism in cultured skin fibroblasts from patients with "neuronal" ceroid lipofuscinosis (Batten's disease).

Authors:  B C Paton; A Poulos
Journal:  J Inherit Metab Dis       Date:  1984       Impact factor: 4.982

4.  Presence of abnormal amounts of dolichols in the urinary sediment of Batten disease patients.

Authors:  N M Kin; L S Wolfe
Journal:  Pediatr Res       Date:  1982-07       Impact factor: 3.756

5.  Dolichol and dolichyl phosphate levels in brain tissue from English setters with ceroid lipofuscinosis.

Authors:  R K Keller; D Armstrong; F C Crum; N Koppang
Journal:  J Neurochem       Date:  1984-04       Impact factor: 5.372

6.  Ceroid lipofuscinosis in sheep. II. The major component of the lipopigment in liver, kidney, pancreas, and brain is low molecular weight protein.

Authors:  D N Palmer; G Barns; D R Husbands; R D Jolly
Journal:  J Biol Chem       Date:  1986-02-05       Impact factor: 5.157

7.  Ceroid lipofuscinosis in sheep. I. Bis(monoacylglycero)phosphate, dolichol, ubiquinone, phospholipids, fatty acids, and fluorescence in liver lipopigment lipids.

Authors:  D N Palmer; D R Husbands; P J Winter; J W Blunt; R D Jolly
Journal:  J Biol Chem       Date:  1986-02-05       Impact factor: 5.157

8.  Dolichols in brain and urinary sediment in neuronal ceroid lipofuscinosis.

Authors:  L S Wolfe; N M Ng Ying Kin; J Palo; M Haltia
Journal:  Neurology       Date:  1983-01       Impact factor: 9.910

9.  Urinary sediment dolichol excretion in patients with Batten disease and other neurodegenerative and storage disorders.

Authors:  M J Bennett; N J Mathers; F W Hemming; I Zweije-Hofman; G P Hosking
Journal:  Pediatr Res       Date:  1985-02       Impact factor: 3.756

10.  Dolichol and phosphorylated dolichol content of tissues in ceroid-lipofuscinosis.

Authors:  N A Hall; A D Patrick
Journal:  J Inherit Metab Dis       Date:  1985       Impact factor: 4.982
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