L Sweetman, W L Nyhan. Show Affiliations »
Abstract
Entities: Chemical
Mesh: See more » Amidohydrolases/deficiencyAnimalsBiotin/deficiencyBiotin/historyBiotin/physiologyBiotin/therapeutic useBiotinidaseCarbon-Carbon LigasesCarbon-Nitrogen LigasesDietHistory, 20th CenturyHumansLigases/deficiencyLigases/geneticsMetabolism, Inborn Errors/diagnosisMetabolism, Inborn Errors/drug therapyMetabolism, Inborn Errors/geneticsMitochondria/enzymologyMutationNutritional RequirementsPyruvate Carboxylase Deficiency Disease
Substances: See more » BiotinAmidohydrolasesBiotinidaseLigasesCarbon-Nitrogen Ligasesholocarboxylase synthetasesCarbon-Carbon Ligasespropionyl CoA carboxylase (ATP-hydrolyzing)methylcrotonoyl-CoA carboxylase
Year: 1986 PMID: 3089241 DOI: 10.1146/annurev.nu.06.070186.001533
Source DB: PubMed Journal: Annu Rev Nutr ISSN: 0199-9885 Impact factor: 11.848